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CASE REPORT Sirosis Hepatis

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CASE REPORT

CASE REPORT

SIROSIS HEPATIS

SIROSIS HEPATIS

Oleh : Oleh : Cintya Naya D 0818011054 Cintya Naya D 0818011054 Gunawan Nata K 0818011062 Gunawan Nata K 0818011062 Preceptor : Preceptor :

dr. Cecep Sulaiman I., Sp. PD dr. Cecep Sulaiman I., Sp. PD

SMF PENYAKIT DALAM

SMF PENYAKIT DALAM

RSUD J

RSUD JENDERAL AHMAD Y

ENDERAL AHMAD YANI M

ANI METRO

ETRO

SEPTEMBER 2012

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CASE REPORT

CASE REPORT

T

Tanggaanggal Masuk Rumah Sal Masuk Rumah Sakitkit : 26-08-2: 26-08-2012012 Pukul

Pukul : : 08.45 08.45 WIBWIB

R

Ruuaannggaann : : SSaaddeewwa a 22

A.

A. ANANAMAMNENESISISS D

Diiaammbbiil l ddaarrii : : AAuuttooaannaammnneessiiss 1.

1. IdIdenentititatass  Nama Pasien

 Nama Pasien : Tn. : Tn. AA Jenis Kelamin : Laki-laki Jenis Kelamin : Laki-laki U

Ummuurr : : 338 8 ttaahhuunn A

Aggaammaa : : IIssllaamm S

Suukkuu : : PPaalleemmbbaanngg P

Peekkeerrjjaaaann : : SSuuppiir  r   A

Allaammaatt : : SSuukkaannaannttii, , NNaattaar  r  

2

2.. RRiiwwaayyaat t PPeennyyaakkiitt

Keluhan Utama Keluhan Utama

Muntah darah seperti gumpalan sebanyak 2x, BAB lembek berwarna Muntah darah seperti gumpalan sebanyak 2x, BAB lembek berwarna hitam seperti aspal.

hitam seperti aspal.

b.

b. KeKeluluhahan Tn Tamambabahahann

Sakit perut 1 malam sebelum masuk RS, perut terasa kembung, sesak, Sakit perut 1 malam sebelum masuk RS, perut terasa kembung, sesak, BAK seperti teh.

BAK seperti teh.

c.

c. RiRiwawayayat Pet Penynyakakit Seit Sekakararangng

Pasien datang dengan keluhan muntah darah sebanyak 2x sejak 1 hari Pasien datang dengan keluhan muntah darah sebanyak 2x sejak 1 hari sebelu

sebelum m masuk rumah sakit. Darah berwarna merah masuk rumah sakit. Darah berwarna merah segar dan segar dan terdapterdapatat gu

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mengatakan sudah pernah dirawat di RSAY dalam satu tahun terakhir  mengatakan sudah pernah dirawat di RSAY dalam satu tahun terakhir  sebanyak 2x dengan keluhan badan terasa lemas, wajah pucat dan cepat sebanyak 2x dengan keluhan badan terasa lemas, wajah pucat dan cepat lelah dalam setiap melakukan kegiatan serta 1x dengan keluhan muntah lelah dalam setiap melakukan kegiatan serta 1x dengan keluhan muntah da

darah rah ununtutuk k yayang ng pepertrtama ama kakalilinynya. a. PaPasiesien n memengngataatakakan n seksekaraarangng merupakan keempat kalinya dirawat di rumah sakit dengan keluhan merupakan keempat kalinya dirawat di rumah sakit dengan keluhan muntah darah dan BAB hitam seperti aspal. Selain itu perut dirasakan muntah darah dan BAB hitam seperti aspal. Selain itu perut dirasakan mu

mulai lai kemkembunbung g dan terus dan terus memmembesabesar r sejasejak k 1 1 bulbulan an teraterakhikhirr, , teraterasasa tegang dan juga keras, kemudian nafas terasa sesak. Pasien menyangkal tegang dan juga keras, kemudian nafas terasa sesak. Pasien menyangkal ka

kaki ki pepernrnah ah bebengngkakak-k-bebengngkakak. k. SeSelamlama a didirarawawat t di di RSRSAAYY, , papasisienen me

mengngakaku u selselalalu u menmendadapapatktkan an tratransnsfufusi si dadarahrah. . PaPasiesien n memengngakakuu mempunyai riwayat mengkonsumsi alkohol sejak usia muda selama mempunyai riwayat mengkonsumsi alkohol sejak usia muda selama lebih dari 5 tahun. Pasien juga mengaku jarang mengkonsumsi lebih dari 5 tahun. Pasien juga mengaku jarang mengkonsumsi obat-obata

obatan n ataupataupun un minum jamu-jamuaminum jamu-jamuan. n. RiwayRiwayat at hiperhipertensi tensi disangdisangkal,kal, riwayat diabetes melitus disangkal, riwayat penyakit jantung disangkal, riwayat diabetes melitus disangkal, riwayat penyakit jantung disangkal, riwayat penyakit kuning disangkal.

riwayat penyakit kuning disangkal.

d.

d. RiwRiwayaayat t PePenyanyakit kit DahDahuluulu

Pasien mengatakan dalam 1 tahun terakhir sudah 3x dirawat di RSAY Pasien mengatakan dalam 1 tahun terakhir sudah 3x dirawat di RSAY ka

karenrena a memendnderierita ta ananememiaia. . RiRiwaywayat at hihipepertrtenensi si didisansangkgkal, al, ririwaywayatat diabetes melitus disangkal, riwayat hepatitis disangkal.

diabetes melitus disangkal, riwayat hepatitis disangkal.

e.

e. RiRiwawayayat Pet Penynyakakit Kit Keleluauargrgaa Pasien menyang

Pasien menyangkal kal bahwa di bahwa di keluarkeluarganyganya a terdapterdapat at riwayriwayat at penyapenyakitkit yang sama.

yang sama.

B.

B. PEMEPEMERIKSRIKSAAN AAN FISIK FISIK (26/(26/AgusAgustus/2tus/2012)012) 1

1.. SSttaattuus s pprreesseenntt K

Keeaaddaaaan Un Ummuumm : : TTaammppaak k ssaakkiit st seeddaanngg K

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T

Teekkaannaan n DDaarraahh : : 112200//660 0 mmmmHHgg  Nadi

 Nadi : 96 x/menit, regular,: 96 x/menit, regular, P

Peerrnnaappaassaann : : 223 3 xx//mmeenniitt S

Suuhhuu : : 3366,,55ooCC

K

Keeaaddaaaan n GGiizzii : ccu: ukkuupp

2.

2. StStatatus us GeGeneneraraliliss Kulit

Kulit W

Waarrnnaa : : ssaawwo o mmaattaanngg E

Efflloorreesseennssii : : ttiiddaak k ddiitteemmuukkaann JJaarriinnggaan n ppaarruutt : : ttiiddaak k ddiitteemmuukkaann P

Piiggmmeennttaassii : : ttiiddaak k ddiitteemmuukkaann Pert

Pertumbumbuhauhan ramn rambutbut : dala: dalam batm batas noras normalmal Pe

Pemmbbululuuh dh dararahah : te: terlrlihihat at di di exextrtrememititasas, t, tererlilihahat dt di abi abdodomemenn S

Suuhhu u rraabbaa : : ddaallaam m bbaattaas s nnoorrmmaall L

Leemmbbaabb//kkeerriinngg : : kkeerriinngg L

Laappiissaan n lleemmaakk : : ttiippiiss IIkktteerruuss : : ppoossiittiif  f   E

Eddeemmaa : : ttiiddaak k ddiitteemmuukkaann

3.

3. KeKelelenjnjar ar GeGetatah Beh Beniningng Submandibula

Submandibula : : tidak tidak teraba teraba pembesaranpembesaran S

Suupprraaccllaavviiccuullaa : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann L

Liippaat t ppaahhaa : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann L

Leehheerr : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann Ketiak

Ketiak : : tidak tidak teraba teraba pembesaranpembesaran

4

4.. KKeeppaallaa E

Ekksspprreessi i wwaajjaahh : : wwaajjaar  r   R

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5

5.. MMaattaa E

Exxoopptthhaallmmuuss : : ttiiddaak k aaddaa E

Ennoopptthhaallmmuuss : : ttiiddaak k aaddaa K

Keellooppaakk : : ooeeddeem m ((--)), , llaasseerraassi i ((--)) L

Leennssaa : : jjeerrnniihh Ko

Konjnjununctctiviva a ananememisis : : +/+/++ S

Skklleerraa aanniikktteerriikk : : ++//++ G

Geerraakkaan n mmaattaa : b: baaiik k kke e sseeggaalla a aarraahh T

Teekkaannan an bboolla ma matataa : N: Noormrmalal De

Devviaiatitio ko koonjnjuugagaee : t: tididak ak diditetemmuukakann  Nystagmus

 Nystagmus : tidak ditemukan: tidak ditemukan

6

6.. TTeelliinnggaa T

Tuullii : : ttiiddaak k aaddaa Selaput

Selaput pendengaran pendengaran : : tidak tidak diperiksadiperiksa Lubang

Lubang : : liang liang lapanglapang P

Peennyyuummbbaattaann : : ttiiddaak k aaddaa P

Peerrddaarraahhaann : : ttiiddaak k aaddaa Cairan

Cairan : : tidak tidak adaada

7

7.. MMuulluutt B

Biibbiirr : : ssiiaannoossiiss, , kkeerriinngg L

Laannggiitt--llaannggiitt : : ttiiddaak k aadda a kkeellaaiinnaann G

Giiggi i ggeelliiggii : : ccaarriieess((++)), , ppllaakk((--)) F

Faarriinngg : : ttiiddaak k hhiippeerreemmiiss L

Liiddaahh : : aattrrooppi i ppaappiil l lliiddaahh T

Toonnssiill : : TT11--TT1 1 tteennaanngg B

Baau u ppeerrnnaappaassaann : : ddaallaam m bbaattaas s nnoorrmmaall Trismus

Trismus : : tidak tidak ditemukanditemukan S

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8

8.. LLeehheerr K

Keelleennjjaar r ttiirrooiidd : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann K

Keelleennjjaar lr liimmffee : t: tiiddaak k tteerraabba a ppeemmbbeessaarraann T

Tekanan vena jugularis: dalaekanan vena jugularis: dalam batas normalm batas normal

9

9.. DDaaddaa B

Beennttuukk : : ssiimmeettrriiss P

Peemmbbuulluuh h ddaarraahh : : nnoorrmmaall

10.

10. PaParu-ru-PaParuru Anterior dan Anterior dan Posterior Posterior K Kaannaann KKiirrii Inspeksi

Inspeksi HHeemmiitthhoorraakks ss siimmeettrriiss HHeemmiitthhoorraax sx siimmeettrriiss Palpasi

Palpasi Fremitus vokal dan taktilFremitus vokal dan taktil simetris

simetris

Fremitus vokal dan taktil Fremitus vokal dan taktil simetris

simetris Perkusi

Perkusi SSoonnoorr SSoonnoorr   

Auskultasi

Auskultasi Anterior : Vesikuler Anterior : Vesikuler 

ronkhi -ronkhi - --wheezing (-) wheezing (-)

Posterior : vesikuler ronkhi Posterior : vesikuler ronkhi + + + + + +

wheezing (-) pada bagian wheezing (-) pada bagian superior, medial dan inferior  superior, medial dan inferior 

Anterior : Vesikuler  Anterior : Vesikuler  ronkhi -ronkhi - --wheezing (-) wheezing (-) Posterior : vesikuler  Posterior : vesikuler  ronkhi + ronkhi + + + + +

wheezing (-) pada bagian wheezing (-) pada bagian superior, medial dan inferior  superior, medial dan inferior  1

11.1. JanJantuntungg

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Batas bawa

Batas bawah jantunh jantungg : ICS IV: ICS IV Batas

Batas kanan kanan jantujantungng : lin: linea parea parasternalasternalis deis dextra xtra ICS ICS IVIV Ba

Batas tas kikiri ri janjantutungng : lin: linea ea mimidcldclavaviciculula sa sininististra ra ICICS S VV Au

Auskskulultatasisi : Bu: Bunynyi Jani Jantutung ng I daI dan II n II regreguleulerr, mu, murmrmur (ur (-), -), gagallollop (-p (-))

12.

12. AbdAbdomeomenn Inspeksi

Inspeksi : : CembungCembung

Palpasi

Palpasi : : Dinding Dinding perut perut : : NTE NTE (+)(+) Hati

Hati : : tidak tidak terabateraba Limpa

Limpa : : schuffner schuffner 22 Ginjal

Ginjal : : sulit sulit di di rabaraba P

Peerrkkuussii : : AAssiittees s ((++)) A

Auusskkuullttaassii : : BBU U ((++) ) nnoorrmmaall R

Reefflleekks s ddiinnddiinng g ppeerruutt : : DDiisstteennssi i ((++))

13.

13. GeniGenitalia Ekstalia Eksternternaa Tidak dilakukan Tidak dilakukan

14.

14. AnggAnggota ota GeraGerak k  L

Leennggaann KKaannaann KKiirrii

Otot

Otot  Normal  Normal NormalNormal

Tonus

Tonus  Normotonus  Normotonus NormotonusNormotonus Massa

Massa Eutrofi Eutrofi EutrofiEutrofi

Sendi

Sendi  Nyeri(-), bengkak (-) Nyeri(-), bengkak (-) Nyeri(-), bengkak (-)Nyeri(-), bengkak (-) Gerakan

Gerakan Aktif Aktif Aktif Aktif 

Kekuatan

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15.

15. ColColok Dubok Duburur Tidak dilakukan Tidak dilakukan

C.

C. PEPEMEMERIRIKSKSAAAAN N PEPENUNUNJNJANANGG 1

1.. LLaabboorraattoorriiuumm Hematologi Hematologi

2

266--0088--1122 3030--0088--1122 3311--0088--1122 NNiillaai i nnoorrmmaall WBC WBC RBC RBC Hb Hb Hct Hct MCV MCV MCH MCH MCHC MCHC PL PLTT LED LED 3,3 3,3 1,26 1,26 2,5 2,5 9,5 9,5 75,5 75,5 19,8 19,8 26,3 26,3 108 108 --1,9 1,9 2,51 2,51 5,5 5,5 17,7 17,7 70,7 70,7 21,9 21,9 31,1 31,1 130 130 20 20 5000-10000/uL 5000-10000/uL 4,37-5,63 jt/uL 4,37-5,63 jt/uL 14-18 g/dL 14-18 g/dL 41-54% 41-54% 80-92 fl 80-92 fl 27-31 pg 27-31 pg 32-36 g/dL 32-36 g/dL 150-450rb/uL 150-450rb/uL L < 10mm/jam L < 10mm/jam

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Cancel Anytime. Albumin Albumin SGPT SGPT Alk.pospat Alk.pospat Bil.indirect Bil.indirect Bil.direct Bil.direct Bil total Bil total Kreatinin Kreatinin Gamma.GT Gamma.GT Globulin Globulin Glikosa Glikosa Protein Protein SGOT SGOT Ureum Ureum 2,40 2,40 15,8 15,8 79,7 79,7 1,34 1,34 0,30 0,30 1,64 1,64 0,96 0,96 29,3 29,3 2,87 2,87 156,4 156,4 5,27 5,27 44,0 44,0 48,5 48,5 2 2,,9922 33,,55--55,,2 2 gg//ddLL 5,0-41,0 U/L 5,0-41,0 U/L 42-128 U/L 42-128 U/L 0,00-0,70 mg/dL 0,00-0,70 mg/dL 0,00-0,20 mg/dL 0,00-0,20 mg/dL 0,10-1,20 mg/dL 0,10-1,20 mg/dL 0,90-1,30 mg/dL 0,90-1,30 mg/dL 5,0-49,0 U/L 5,0-49,0 U/L 2,0-3,5 g/dL 2,0-3,5 g/dL 70,0-109,0 70,0-109,0 mg/dL mg/dL 6,60-8,80 g/dL 6,60-8,80 g/dL 5,0-35,0 g/dL 5,0-35,0 g/dL 17,0-43,0 mg/dL 17,0-43,0 mg/dL Serologi

Serologi (19 (19 Juli Juli 2012)2012)

JJeenniis s PPeemmeerriikkssaaaann HHaassiill NNiillaai i NNoorrmmaall HbsAg

HbsAg Anti HAV IgM Anti HAV IgM

 Non Reaktif   Non Reaktif   Non Reaktif   Non Reaktif   Non Reaktif   Non Reaktif   Non Reaktif   Non Reaktif  Analisa Cairan

Analisa Cairan Asites Asites (29 (29 Agustus 2012)Agustus 2012)

JJeenniis s PPeemmeerriikkssaaaann HHaassiill NNiillaai i NNoorrmmaall Protein Total Cairan

Protein Total Cairan Protein Total Serum Protein Total Serum

Ratio Ratio 0,54 g/dL 0,54 g/dL 0,6 g/dL 0,6 g/dL 0,09 0,09 6,6-8,8 6,6-8,8 < 0,5 < 0,5

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S

SAAAAGG 22,,3388

Kesimpulan: Sifat cairan asites adalah transudat dengan nilai SAAG > 1,1 Kesimpulan: Sifat cairan asites adalah transudat dengan nilai SAAG > 1,1 g/dL (berhubungan dengan hipertensi portal)

g/dL (berhubungan dengan hipertensi portal)

Endoskopi

Endoskopi (24-07-2012)(24-07-2012)

USG (12-07-2012) USG (12-07-2012)

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D.

D. DIDIAGAGNONOSISIS S KEKERJRJAA Sirosis Hepatis

Sirosis Hepatis

DIAGNOSIS BANDING DIAGNOSIS BANDING

PEMERIKSAAN YANG DIANJURKAN PEMERIKSAAN YANG DIANJURKAN Biopsi Hepar 

Biopsi Hepar  G.

G. RENCARENCANA NA PENGEPENGELOLAALOLAAN (TN (Teraperapi Ruai Ruangan)ngan) -- PrPro to traransnsfufusi si sasampmpai ai Hb Hb > 1> 10 g0 gr/r/dLdL

-- IVIVFFD D D D 5% 5% xx xx tetetetes ps per er memeninitt -- AmAmininoofufusisin n InInjejeksksi i 1x1x11

-- AsAsam am TTrarannekeksasammat at peper 8 r 8 jajamm

-- Amoksicilin 3 x 500 gr Amoksicilin 3 x 500 gr 

-- LLaannssoopprarazzoolle 1 e 1 x x 1 t1 taabb

-- Metochlopramid 2 x 1 ampulMetochlopramid 2 x 1 ampul

-- PProroppaannoollool 3 l 3 x 1x 10 g0 gr Pr POO V

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FOLLOW UP FOLLOW UP TANGGAL

TANGGAL 27 Agustus 201227 Agustus 2012

Keluhan:

Keluhan: •• Sesak Sesak 

• Kembung (+)Kembung (+) •

• Muntah darah (+) 1 kaliMuntah darah (+) 1 kali • • Lemas (+)Lemas (+) • • takikardi (+)takikardi (+) Pemeriksaan Fisik  Pemeriksaan Fisik  Kesadaran Kesadaran Keadaan Umum Keadaan Umum 

 Vital SignVital Sign - TD - TD - Nadi - Nadi - RR  - RR  - Suhu - Suhu • • CACA • • SISI •

• Compos mentisCompos mentis •

• TTampak sakit ampak sakit sedangsedang

• • 110/60 mmHg110/60 mmHg • • 120 x/mnt120 x/mnt • • 20 x/mnt20 x/mnt • • 36,036,0 °°CC • • +/++/+ • • +/++/+

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• Muntah darah (-)Muntah darah (-) • • takikardi (-)takikardi (-) Pemeriksaan Fisik  Pemeriksaan Fisik  Kesadaran Kesadaran Keadaan Umum Keadaan Umum 

 Vital SignVital Sign - TD - TD - Nadi - Nadi - RR  - RR  - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung Abdomen Abdomen •

• Compos mentisCompos mentis •

• TTampak sakit ampak sakit sedangsedang

• • 100/50 mmHg100/50 mmHg • • 92 x/mnt92 x/mnt • • 32 x/mnt32 x/mnt • • 37,037,0 °°CC • • +/++/+ • • +/++/+ •

• Atropi papil lidahAtropi papil lidah •

• SimetrisSimetris •

• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •

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Cancel Anytime. Pemeriksaan Fisik  Pemeriksaan Fisik  Kesadaran Kesadaran Keadaan Umum Keadaan Umum 

 Vital SignVital Sign - TD - TD - Nadi - Nadi - RR  - RR  - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • • • EkstremitasEkstremitas •

• Compos mentisCompos mentis •

• TTampak sakit ampak sakit sedangsedang

• • 120/70 mmHg120/70 mmHg • • 100 x/mnt100 x/mnt • • 32 x/mnt32 x/mnt • • 36,436,4 °°CC • • +/++/+ • • +/++/+ •

• Atropi papil lidahAtropi papil lidah •

• SimetrisSimetris •

• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •

• BJ I II reguler, murmur (-), gallop (-)BJ I II reguler, murmur (-), gallop (-) •

• Cembung, asites (+), lien teraba diCembung, asites (+), lien teraba di

schuffner 2, hepar tidak teraba. schuffner 2, hepar tidak teraba.

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Cancel Anytime. - Nadi - Nadi - RR  - RR  - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • • • EkstremitasEkstremitas • • 100 x/mnt100 x/mnt • • 24 x/mnt24 x/mnt • • 35,535,5 °°CC • • +/++/+ • • +/++/+ •

• Atropi papil lidahAtropi papil lidah •

• SimetrisSimetris •

• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •

• BJ I II reguler, murmur (-), gallop (-)BJ I II reguler, murmur (-), gallop (-) •

• Cembung, asites (+), lien teraba diCembung, asites (+), lien teraba di

schuffner 2, hepar tidak teraba. schuffner 2, hepar tidak teraba.

• Edema ekstremitas (-)Edema ekstremitas (-) •

• Kuku sendok (+)Kuku sendok (+)

TANGGAL

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Cancel Anytime. • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • EkstremitasEkstremitas +/+ +/+

Atropi papil lidah Atropi papil lidah Simetris

Simetris V

Vesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) BJ I II reguler, murmur (-), gallop (-)

BJ I II reguler, murmur (-), gallop (-)

Cembung, asites (+), lien teraba di schuffner 2, Cembung, asites (+), lien teraba di schuffner 2, hepar tidak teraba.

hepar tidak teraba. Edema ekstremitas (-) Edema ekstremitas (-) Kuku sendok (+) Kuku sendok (+)

TANGGAL

TANGGAL 31 Agustus 201231 Agustus 2012

Keluhan:

Keluhan: •• Sesak nafas (-)Sesak nafas (-) •

• Batuk berdahak (+)Batuk berdahak (+)

Pemeriksaan Fisik  Pemeriksaan Fisik  Kesadaran Kesadaran Keadaan Umum Keadaan Umum 

 Vital SignVital Sign

• Compos mentisCompos mentis •

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2

2.. ApApakakah ah didiagagnonosisis ps padada ka kasasuus is ini ni susuddah ah tetepapat?t? Di

Diagagnnoosisis s ppadada a kkasasuus s inini i susudadah h tetepapat t beberdrdasasararkkan an ananamamnenesisis,s,  pemeriksaan fisik

 pemeriksaan fisik dan pemeriksaan dan pemeriksaan penunjang yang telah penunjang yang telah dilakukan. Daridilakukan. Dari anamnesis diketahui bahwa pasien pernah mengkonsumsi alkohol dalam anamnesis diketahui bahwa pasien pernah mengkonsumsi alkohol dalam waktu lama, mengalami muntah darah (hematemesis) dan BAB hitam waktu lama, mengalami muntah darah (hematemesis) dan BAB hitam (melen

(melena), a), perut teraperut terasa kembunsa kembung dan semakin lamg dan semakin lama semakin mema semakin membesar besar  (a

(asciscitetes) s) sehsehiningggga a terterasa asa sessesakak. . PaPada da pempemerieriksksaaaan n fifisik sik dididadapatpatkakann  pembesaran lien (splenomegali),

 pembesaran lien (splenomegali), penumpukan cairan di rongga peritonealpenumpukan cairan di rongga peritoneal (ascites), konjungtiva anemis, sclera ikterik. Pada pemeriksaan penunjang (ascites), konjungtiva anemis, sclera ikterik. Pada pemeriksaan penunjang di

ditemtemukukan an pepenunururunanan n alalbubumimin, n, USUSG G ababdodomemen n yayang ng memenununjnjukukkakann karakteristik sirosis hepatis.

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teratur dan terjadi penambahan jaringan ikat (fibrosis) di sekitar parenkim hati teratur dan terjadi penambahan jaringan ikat (fibrosis) di sekitar parenkim hati yang mengalami regenerasi.

yang mengalami regenerasi.

Insidens Insidens Pe

Pendndereritita a sisirorosisis s hahati ti lelebibih h babanynyak ak didijujumpmpai ai papada da kakaum um lalakiki-l-lakaki i jijikaka dibandingkan dengan kaum wanita sekita 1,6 : 1 dengan umur rata-rata terbanyak  dibandingkan dengan kaum wanita sekita 1,6 : 1 dengan umur rata-rata terbanyak  antara golongan umur 30 – 59 ta

antara golongan umur 30 – 59 tahun dengan puncaknya sekitar 40 – hun dengan puncaknya sekitar 40 – 449 tahun.449 tahun.

Klasifikasi Klasifikasi

Berdasarkan morfologi Sherlock membagi Sirosis hati atas 3 jenis, yaitu : Berdasarkan morfologi Sherlock membagi Sirosis hati atas 3 jenis, yaitu : 1

1.. MMiikkrroonnoodduullaar r  2

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4

4.. GlGlikikoononosisis s tytyppe-e-IVIV 5

5.. GGaallaakkttoosseemmiiaa 6

6.. TTiirroossiinneemmiiaa 7

7.. KKoolleessttaassiiss

Saluran empedu membawa empedu yang dihasilkan oleh hati ke usus, dimana Saluran empedu membawa empedu yang dihasilkan oleh hati ke usus, dimana empedu membantu mencerna lemak. Pada bayi penyebab sirosis terbanyak  empedu membantu mencerna lemak. Pada bayi penyebab sirosis terbanyak  adalah akibat tersumbatnya saluran empedu yang disebut Biliary atresia. Pada adalah akibat tersumbatnya saluran empedu yang disebut Biliary atresia. Pada  penyakit

 penyakit ini ini empedumemenuhi empedumemenuhi hati hati karena karena saluran saluran empedu empedu tidak tidak berfungsiberfungsi atau

atau rusrusak. ak. BayBayi i yanyang g menmenderiderita ta BilBiliary iary berberwarnwarna a kunkuning ing (ku(kulit lit kunkuninging)) setelah berusia satu bulan. Kadang bisa diatasi dengan pembedahan untuk  setelah berusia satu bulan. Kadang bisa diatasi dengan pembedahan untuk  membentuk saluran baru agar empedu meninggalkan hati, tetapi transplantasi membentuk saluran baru agar empedu meninggalkan hati, tetapi transplantasi diindikasikan untuk anak-anak yang menderita penyakit hati stadium akhir. diindikasikan untuk anak-anak yang menderita penyakit hati stadium akhir.

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3

3.. AAssiitteess 4.

4. EnEnsesefafalolophphatati hi hepepatatititisis

Keluhan dari sirosis hati dapat berupa : Keluhan dari sirosis hati dapat berupa : a.

a. MerMerasa asa kekemamampmpuauan jn jasmasmanani mi menenururunun  b.

 b. Nausea, nafsu makan menurun dan diikuti dengNausea, nafsu makan menurun dan diikuti dengan penurunan berat badanan penurunan berat badan c.

c. Mata Mata berberwarnwarna kua kuninning dag dan bn buanuang aig air ker kecil bcil berwerwarnarna gea gelaplap d.

d. PemPembebesarsaran pan peruerut dat dan kn kakaki bi benengkgkak ak  e.

e. PePerdrdararahaahan sn salalururan an cercerna na babagigian an atatasas aa

aaPadPada a keakeadaan daan lanlanjut jut dapdapat at dijdijumpumpai ai pasipasien en tidtidak ak sadasadarkarkan n dirdiri i (He(Hepatpaticic Enchephalopathy)

Enchephalopathy) g.

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 b.

 b. spleenomegalispleenomegali aa

aa  perubahan sumsum tulang perubahan sumsum tulang aa

aa caput medusacaput medusa ee.. aassiitteess

ff.. ccoollllaatteerraal l vveeiinnhheemmoorrrrhhooiidd g

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Penatalaksanaan Penatalaksanaan

Pengobatan sirosis hati pada prinsipnya berupa : Pengobatan sirosis hati pada prinsipnya berupa : 1

1.. SSiimmttoommaattiiss 2

2.. SuSupppporortitif, f, yyaiaitu tu :: a.

a. IstiIstirahrahat yat yang ang cukcukupup aa

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Pemberian diuretic hanya bagi penderita yang telah menjalani diet rendah Pemberian diuretic hanya bagi penderita yang telah menjalani diet rendah garam dan pembatasan cairan namun penurunan berat badannya kurang garam dan pembatasan cairan namun penurunan berat badannya kurang dari 1 kg setelah 4 hari. Mengingat salah satu komplikasi akibat pemberian dari 1 kg setelah 4 hari. Mengingat salah satu komplikasi akibat pemberian diuretic adala hipokalemia dan hal ini dapat mencetuskan encepalophaty diuretic adala hipokalemia dan hal ini dapat mencetuskan encepalophaty hepatic, maka pilihan utama diuretic adalah spironolacton, dan dimulai hepatic, maka pilihan utama diuretic adalah spironolacton, dan dimulai dengan dosis rendah, serta dapat dinaikkan dosisnya bertahap tiap 3-4 hari, dengan dosis rendah, serta dapat dinaikkan dosisnya bertahap tiap 3-4 hari,

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o

o Start antibiotic if ascites > 250 mm polymorphsStart antibiotic if ascites > 250 mm polymorphs

o

o 50% die50% die

o

o 69 % recure in 1 year 69 % recure in 1 year 

Pe

Pengngobobataatan n SBSBP P dedengngan an memembmberierikakan n CeCephphaloalosposporirins ns GeGenenerasrasi i IIIIII (Cefotaxime), secara parental selama lima hari, atau Qinolon secara oral. (Cefotaxime), secara parental selama lima hari, atau Qinolon secara oral. Mengi

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 pasien

 pasien yang yang akan akan dilakukan dilakukan transplantasi. transplantasi. Pilihan Pilihan terbaik terbaik adalahadalah transplantasi hati yang diikuti dengan perbaikan dan fungsi ginjal.

transplantasi hati yang diikuti dengan perbaikan dan fungsi ginjal.

Ensefalophaty hepatic Ensefalophaty hepatic

Suatu sindrom neuropsikiatri yang didapatkan pada penderita penyakit hati Suatu sindrom neuropsikiatri yang didapatkan pada penderita penyakit hati menahun, mulai dari gangguan ritme tidur, perubahan kepribadian, gelisah menahun, mulai dari gangguan ritme tidur, perubahan kepribadian, gelisah

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