CASE REPORT
CASE REPORT
SIROSIS HEPATIS
SIROSIS HEPATIS
Oleh : Oleh : Cintya Naya D 0818011054 Cintya Naya D 0818011054 Gunawan Nata K 0818011062 Gunawan Nata K 0818011062 Preceptor : Preceptor :dr. Cecep Sulaiman I., Sp. PD dr. Cecep Sulaiman I., Sp. PD
SMF PENYAKIT DALAM
SMF PENYAKIT DALAM
RSUD J
RSUD JENDERAL AHMAD Y
ENDERAL AHMAD YANI M
ANI METRO
ETRO
SEPTEMBER 2012
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CASE REPORT
CASE REPORT
T
Tanggaanggal Masuk Rumah Sal Masuk Rumah Sakitkit : 26-08-2: 26-08-2012012 Pukul
Pukul : : 08.45 08.45 WIBWIB
R
Ruuaannggaann : : SSaaddeewwa a 22
A.
A. ANANAMAMNENESISISS D
Diiaammbbiil l ddaarrii : : AAuuttooaannaammnneessiiss 1.
1. IdIdenentititatass Nama Pasien
Nama Pasien : Tn. : Tn. AA Jenis Kelamin : Laki-laki Jenis Kelamin : Laki-laki U
Ummuurr : : 338 8 ttaahhuunn A
Aggaammaa : : IIssllaamm S
Suukkuu : : PPaalleemmbbaanngg P
Peekkeerrjjaaaann : : SSuuppiir r A
Allaammaatt : : SSuukkaannaannttii, , NNaattaar r
2
2.. RRiiwwaayyaat t PPeennyyaakkiitt
Keluhan Utama Keluhan Utama
Muntah darah seperti gumpalan sebanyak 2x, BAB lembek berwarna Muntah darah seperti gumpalan sebanyak 2x, BAB lembek berwarna hitam seperti aspal.
hitam seperti aspal.
b.
b. KeKeluluhahan Tn Tamambabahahann
Sakit perut 1 malam sebelum masuk RS, perut terasa kembung, sesak, Sakit perut 1 malam sebelum masuk RS, perut terasa kembung, sesak, BAK seperti teh.
BAK seperti teh.
c.
c. RiRiwawayayat Pet Penynyakakit Seit Sekakararangng
Pasien datang dengan keluhan muntah darah sebanyak 2x sejak 1 hari Pasien datang dengan keluhan muntah darah sebanyak 2x sejak 1 hari sebelu
sebelum m masuk rumah sakit. Darah berwarna merah masuk rumah sakit. Darah berwarna merah segar dan segar dan terdapterdapatat gu
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mengatakan sudah pernah dirawat di RSAY dalam satu tahun terakhir mengatakan sudah pernah dirawat di RSAY dalam satu tahun terakhir sebanyak 2x dengan keluhan badan terasa lemas, wajah pucat dan cepat sebanyak 2x dengan keluhan badan terasa lemas, wajah pucat dan cepat lelah dalam setiap melakukan kegiatan serta 1x dengan keluhan muntah lelah dalam setiap melakukan kegiatan serta 1x dengan keluhan muntah da
darah rah ununtutuk k yayang ng pepertrtama ama kakalilinynya. a. PaPasiesien n memengngataatakakan n seksekaraarangng merupakan keempat kalinya dirawat di rumah sakit dengan keluhan merupakan keempat kalinya dirawat di rumah sakit dengan keluhan muntah darah dan BAB hitam seperti aspal. Selain itu perut dirasakan muntah darah dan BAB hitam seperti aspal. Selain itu perut dirasakan mu
mulai lai kemkembunbung g dan terus dan terus memmembesabesar r sejasejak k 1 1 bulbulan an teraterakhikhirr, , teraterasasa tegang dan juga keras, kemudian nafas terasa sesak. Pasien menyangkal tegang dan juga keras, kemudian nafas terasa sesak. Pasien menyangkal ka
kaki ki pepernrnah ah bebengngkakak-k-bebengngkakak. k. SeSelamlama a didirarawawat t di di RSRSAAYY, , papasisienen me
mengngakaku u selselalalu u menmendadapapatktkan an tratransnsfufusi si dadarahrah. . PaPasiesien n memengngakakuu mempunyai riwayat mengkonsumsi alkohol sejak usia muda selama mempunyai riwayat mengkonsumsi alkohol sejak usia muda selama lebih dari 5 tahun. Pasien juga mengaku jarang mengkonsumsi lebih dari 5 tahun. Pasien juga mengaku jarang mengkonsumsi obat-obata
obatan n ataupataupun un minum jamu-jamuaminum jamu-jamuan. n. RiwayRiwayat at hiperhipertensi tensi disangdisangkal,kal, riwayat diabetes melitus disangkal, riwayat penyakit jantung disangkal, riwayat diabetes melitus disangkal, riwayat penyakit jantung disangkal, riwayat penyakit kuning disangkal.
riwayat penyakit kuning disangkal.
d.
d. RiwRiwayaayat t PePenyanyakit kit DahDahuluulu
Pasien mengatakan dalam 1 tahun terakhir sudah 3x dirawat di RSAY Pasien mengatakan dalam 1 tahun terakhir sudah 3x dirawat di RSAY ka
karenrena a memendnderierita ta ananememiaia. . RiRiwaywayat at hihipepertrtenensi si didisansangkgkal, al, ririwaywayatat diabetes melitus disangkal, riwayat hepatitis disangkal.
diabetes melitus disangkal, riwayat hepatitis disangkal.
e.
e. RiRiwawayayat Pet Penynyakakit Kit Keleluauargrgaa Pasien menyang
Pasien menyangkal kal bahwa di bahwa di keluarkeluarganyganya a terdapterdapat at riwayriwayat at penyapenyakitkit yang sama.
yang sama.
B.
B. PEMEPEMERIKSRIKSAAN AAN FISIK FISIK (26/(26/AgusAgustus/2tus/2012)012) 1
1.. SSttaattuus s pprreesseenntt K
Keeaaddaaaan Un Ummuumm : : TTaammppaak k ssaakkiit st seeddaanngg K
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T
Teekkaannaan n DDaarraahh : : 112200//660 0 mmmmHHgg Nadi
Nadi : 96 x/menit, regular,: 96 x/menit, regular, P
Peerrnnaappaassaann : : 223 3 xx//mmeenniitt S
Suuhhuu : : 3366,,55ooCC
K
Keeaaddaaaan n GGiizzii : ccu: ukkuupp
2.
2. StStatatus us GeGeneneraraliliss Kulit
Kulit W
Waarrnnaa : : ssaawwo o mmaattaanngg E
Efflloorreesseennssii : : ttiiddaak k ddiitteemmuukkaann JJaarriinnggaan n ppaarruutt : : ttiiddaak k ddiitteemmuukkaann P
Piiggmmeennttaassii : : ttiiddaak k ddiitteemmuukkaann Pert
Pertumbumbuhauhan ramn rambutbut : dala: dalam batm batas noras normalmal Pe
Pemmbbululuuh dh dararahah : te: terlrlihihat at di di exextrtrememititasas, t, tererlilihahat dt di abi abdodomemenn S
Suuhhu u rraabbaa : : ddaallaam m bbaattaas s nnoorrmmaall L
Leemmbbaabb//kkeerriinngg : : kkeerriinngg L
Laappiissaan n lleemmaakk : : ttiippiiss IIkktteerruuss : : ppoossiittiif f E
Eddeemmaa : : ttiiddaak k ddiitteemmuukkaann
3.
3. KeKelelenjnjar ar GeGetatah Beh Beniningng Submandibula
Submandibula : : tidak tidak teraba teraba pembesaranpembesaran S
Suupprraaccllaavviiccuullaa : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann L
Liippaat t ppaahhaa : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann L
Leehheerr : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann Ketiak
Ketiak : : tidak tidak teraba teraba pembesaranpembesaran
4
4.. KKeeppaallaa E
Ekksspprreessi i wwaajjaahh : : wwaajjaar r R
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5
5.. MMaattaa E
Exxoopptthhaallmmuuss : : ttiiddaak k aaddaa E
Ennoopptthhaallmmuuss : : ttiiddaak k aaddaa K
Keellooppaakk : : ooeeddeem m ((--)), , llaasseerraassi i ((--)) L
Leennssaa : : jjeerrnniihh Ko
Konjnjununctctiviva a ananememisis : : +/+/++ S
Skklleerraa aanniikktteerriikk : : ++//++ G
Geerraakkaan n mmaattaa : b: baaiik k kke e sseeggaalla a aarraahh T
Teekkaannan an bboolla ma matataa : N: Noormrmalal De
Devviaiatitio ko koonjnjuugagaee : t: tididak ak diditetemmuukakann Nystagmus
Nystagmus : tidak ditemukan: tidak ditemukan
6
6.. TTeelliinnggaa T
Tuullii : : ttiiddaak k aaddaa Selaput
Selaput pendengaran pendengaran : : tidak tidak diperiksadiperiksa Lubang
Lubang : : liang liang lapanglapang P
Peennyyuummbbaattaann : : ttiiddaak k aaddaa P
Peerrddaarraahhaann : : ttiiddaak k aaddaa Cairan
Cairan : : tidak tidak adaada
7
7.. MMuulluutt B
Biibbiirr : : ssiiaannoossiiss, , kkeerriinngg L
Laannggiitt--llaannggiitt : : ttiiddaak k aadda a kkeellaaiinnaann G
Giiggi i ggeelliiggii : : ccaarriieess((++)), , ppllaakk((--)) F
Faarriinngg : : ttiiddaak k hhiippeerreemmiiss L
Liiddaahh : : aattrrooppi i ppaappiil l lliiddaahh T
Toonnssiill : : TT11--TT1 1 tteennaanngg B
Baau u ppeerrnnaappaassaann : : ddaallaam m bbaattaas s nnoorrmmaall Trismus
Trismus : : tidak tidak ditemukanditemukan S
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8
8.. LLeehheerr K
Keelleennjjaar r ttiirrooiidd : : ttiiddaak k tteerraabba a ppeemmbbeessaarraann K
Keelleennjjaar lr liimmffee : t: tiiddaak k tteerraabba a ppeemmbbeessaarraann T
Tekanan vena jugularis: dalaekanan vena jugularis: dalam batas normalm batas normal
9
9.. DDaaddaa B
Beennttuukk : : ssiimmeettrriiss P
Peemmbbuulluuh h ddaarraahh : : nnoorrmmaall
10.
10. PaParu-ru-PaParuru Anterior dan Anterior dan Posterior Posterior K Kaannaann KKiirrii Inspeksi
Inspeksi HHeemmiitthhoorraakks ss siimmeettrriiss HHeemmiitthhoorraax sx siimmeettrriiss Palpasi
Palpasi Fremitus vokal dan taktilFremitus vokal dan taktil simetris
simetris
Fremitus vokal dan taktil Fremitus vokal dan taktil simetris
simetris Perkusi
Perkusi SSoonnoorr SSoonnoorr
Auskultasi
Auskultasi Anterior : Vesikuler Anterior : Vesikuler
ronkhi -ronkhi - --wheezing (-) wheezing (-)
Posterior : vesikuler ronkhi Posterior : vesikuler ronkhi + + + + + +
wheezing (-) pada bagian wheezing (-) pada bagian superior, medial dan inferior superior, medial dan inferior
Anterior : Vesikuler Anterior : Vesikuler ronkhi -ronkhi - --wheezing (-) wheezing (-) Posterior : vesikuler Posterior : vesikuler ronkhi + ronkhi + + + + +
wheezing (-) pada bagian wheezing (-) pada bagian superior, medial dan inferior superior, medial dan inferior 1
11.1. JanJantuntungg
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Batas bawa
Batas bawah jantunh jantungg : ICS IV: ICS IV Batas
Batas kanan kanan jantujantungng : lin: linea parea parasternalasternalis deis dextra xtra ICS ICS IVIV Ba
Batas tas kikiri ri janjantutungng : lin: linea ea mimidcldclavaviciculula sa sininististra ra ICICS S VV Au
Auskskulultatasisi : Bu: Bunynyi Jani Jantutung ng I daI dan II n II regreguleulerr, mu, murmrmur (ur (-), -), gagallollop (-p (-))
12.
12. AbdAbdomeomenn Inspeksi
Inspeksi : : CembungCembung
Palpasi
Palpasi : : Dinding Dinding perut perut : : NTE NTE (+)(+) Hati
Hati : : tidak tidak terabateraba Limpa
Limpa : : schuffner schuffner 22 Ginjal
Ginjal : : sulit sulit di di rabaraba P
Peerrkkuussii : : AAssiittees s ((++)) A
Auusskkuullttaassii : : BBU U ((++) ) nnoorrmmaall R
Reefflleekks s ddiinnddiinng g ppeerruutt : : DDiisstteennssi i ((++))
13.
13. GeniGenitalia Ekstalia Eksternternaa Tidak dilakukan Tidak dilakukan
14.
14. AnggAnggota ota GeraGerak k L
Leennggaann KKaannaann KKiirrii
Otot
Otot Normal Normal NormalNormal
Tonus
Tonus Normotonus Normotonus NormotonusNormotonus Massa
Massa Eutrofi Eutrofi EutrofiEutrofi
Sendi
Sendi Nyeri(-), bengkak (-) Nyeri(-), bengkak (-) Nyeri(-), bengkak (-)Nyeri(-), bengkak (-) Gerakan
Gerakan Aktif Aktif Aktif Aktif
Kekuatan
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15.
15. ColColok Dubok Duburur Tidak dilakukan Tidak dilakukan
C.
C. PEPEMEMERIRIKSKSAAAAN N PEPENUNUNJNJANANGG 1
1.. LLaabboorraattoorriiuumm Hematologi Hematologi
2
266--0088--1122 3030--0088--1122 3311--0088--1122 NNiillaai i nnoorrmmaall WBC WBC RBC RBC Hb Hb Hct Hct MCV MCV MCH MCH MCHC MCHC PL PLTT LED LED 3,3 3,3 1,26 1,26 2,5 2,5 9,5 9,5 75,5 75,5 19,8 19,8 26,3 26,3 108 108 --1,9 1,9 2,51 2,51 5,5 5,5 17,7 17,7 70,7 70,7 21,9 21,9 31,1 31,1 130 130 20 20 5000-10000/uL 5000-10000/uL 4,37-5,63 jt/uL 4,37-5,63 jt/uL 14-18 g/dL 14-18 g/dL 41-54% 41-54% 80-92 fl 80-92 fl 27-31 pg 27-31 pg 32-36 g/dL 32-36 g/dL 150-450rb/uL 150-450rb/uL L < 10mm/jam L < 10mm/jam
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Cancel Anytime. Albumin Albumin SGPT SGPT Alk.pospat Alk.pospat Bil.indirect Bil.indirect Bil.direct Bil.direct Bil total Bil total Kreatinin Kreatinin Gamma.GT Gamma.GT Globulin Globulin Glikosa Glikosa Protein Protein SGOT SGOT Ureum Ureum 2,40 2,40 15,8 15,8 79,7 79,7 1,34 1,34 0,30 0,30 1,64 1,64 0,96 0,96 29,3 29,3 2,87 2,87 156,4 156,4 5,27 5,27 44,0 44,0 48,5 48,5 2 2,,9922 33,,55--55,,2 2 gg//ddLL 5,0-41,0 U/L 5,0-41,0 U/L 42-128 U/L 42-128 U/L 0,00-0,70 mg/dL 0,00-0,70 mg/dL 0,00-0,20 mg/dL 0,00-0,20 mg/dL 0,10-1,20 mg/dL 0,10-1,20 mg/dL 0,90-1,30 mg/dL 0,90-1,30 mg/dL 5,0-49,0 U/L 5,0-49,0 U/L 2,0-3,5 g/dL 2,0-3,5 g/dL 70,0-109,0 70,0-109,0 mg/dL mg/dL 6,60-8,80 g/dL 6,60-8,80 g/dL 5,0-35,0 g/dL 5,0-35,0 g/dL 17,0-43,0 mg/dL 17,0-43,0 mg/dL Serologi
Serologi (19 (19 Juli Juli 2012)2012)
JJeenniis s PPeemmeerriikkssaaaann HHaassiill NNiillaai i NNoorrmmaall HbsAg
HbsAg Anti HAV IgM Anti HAV IgM
Non Reaktif Non Reaktif Non Reaktif Non Reaktif Non Reaktif Non Reaktif Non Reaktif Non Reaktif Analisa Cairan
Analisa Cairan Asites Asites (29 (29 Agustus 2012)Agustus 2012)
JJeenniis s PPeemmeerriikkssaaaann HHaassiill NNiillaai i NNoorrmmaall Protein Total Cairan
Protein Total Cairan Protein Total Serum Protein Total Serum
Ratio Ratio 0,54 g/dL 0,54 g/dL 0,6 g/dL 0,6 g/dL 0,09 0,09 6,6-8,8 6,6-8,8 < 0,5 < 0,5
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S
SAAAAGG 22,,3388
Kesimpulan: Sifat cairan asites adalah transudat dengan nilai SAAG > 1,1 Kesimpulan: Sifat cairan asites adalah transudat dengan nilai SAAG > 1,1 g/dL (berhubungan dengan hipertensi portal)
g/dL (berhubungan dengan hipertensi portal)
Endoskopi
Endoskopi (24-07-2012)(24-07-2012)
USG (12-07-2012) USG (12-07-2012)
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D.
D. DIDIAGAGNONOSISIS S KEKERJRJAA Sirosis Hepatis
Sirosis Hepatis
DIAGNOSIS BANDING DIAGNOSIS BANDING
PEMERIKSAAN YANG DIANJURKAN PEMERIKSAAN YANG DIANJURKAN Biopsi Hepar
Biopsi Hepar G.
G. RENCARENCANA NA PENGEPENGELOLAALOLAAN (TN (Teraperapi Ruai Ruangan)ngan) -- PrPro to traransnsfufusi si sasampmpai ai Hb Hb > 1> 10 g0 gr/r/dLdL
-- IVIVFFD D D D 5% 5% xx xx tetetetes ps per er memeninitt -- AmAmininoofufusisin n InInjejeksksi i 1x1x11
-- AsAsam am TTrarannekeksasammat at peper 8 r 8 jajamm
-- Amoksicilin 3 x 500 gr Amoksicilin 3 x 500 gr
-- LLaannssoopprarazzoolle 1 e 1 x x 1 t1 taabb
-- Metochlopramid 2 x 1 ampulMetochlopramid 2 x 1 ampul
-- PProroppaannoollool 3 l 3 x 1x 10 g0 gr Pr POO V
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FOLLOW UP FOLLOW UP TANGGAL
TANGGAL 27 Agustus 201227 Agustus 2012
Keluhan:
Keluhan: •• Sesak Sesak
•
• Kembung (+)Kembung (+) •
• Muntah darah (+) 1 kaliMuntah darah (+) 1 kali • • Lemas (+)Lemas (+) • • takikardi (+)takikardi (+) Pemeriksaan Fisik Pemeriksaan Fisik Kesadaran Kesadaran Keadaan Umum Keadaan Umum
Vital SignVital Sign - TD - TD - Nadi - Nadi - RR - RR - Suhu - Suhu • • CACA • • SISI •
• Compos mentisCompos mentis •
• TTampak sakit ampak sakit sedangsedang
• • 110/60 mmHg110/60 mmHg • • 120 x/mnt120 x/mnt • • 20 x/mnt20 x/mnt • • 36,036,0 °°CC • • +/++/+ • • +/++/+
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•
• Muntah darah (-)Muntah darah (-) • • takikardi (-)takikardi (-) Pemeriksaan Fisik Pemeriksaan Fisik Kesadaran Kesadaran Keadaan Umum Keadaan Umum
Vital SignVital Sign - TD - TD - Nadi - Nadi - RR - RR - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung Abdomen Abdomen •
• Compos mentisCompos mentis •
• TTampak sakit ampak sakit sedangsedang
• • 100/50 mmHg100/50 mmHg • • 92 x/mnt92 x/mnt • • 32 x/mnt32 x/mnt • • 37,037,0 °°CC • • +/++/+ • • +/++/+ •
• Atropi papil lidahAtropi papil lidah •
• SimetrisSimetris •
• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •
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Cancel Anytime. Pemeriksaan Fisik Pemeriksaan Fisik Kesadaran Kesadaran Keadaan Umum Keadaan Umum
Vital SignVital Sign - TD - TD - Nadi - Nadi - RR - RR - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • • • EkstremitasEkstremitas •
• Compos mentisCompos mentis •
• TTampak sakit ampak sakit sedangsedang
• • 120/70 mmHg120/70 mmHg • • 100 x/mnt100 x/mnt • • 32 x/mnt32 x/mnt • • 36,436,4 °°CC • • +/++/+ • • +/++/+ •
• Atropi papil lidahAtropi papil lidah •
• SimetrisSimetris •
• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •
• BJ I II reguler, murmur (-), gallop (-)BJ I II reguler, murmur (-), gallop (-) •
• Cembung, asites (+), lien teraba diCembung, asites (+), lien teraba di
schuffner 2, hepar tidak teraba. schuffner 2, hepar tidak teraba.
•
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Cancel Anytime. - Nadi - Nadi - RR - RR - Suhu - Suhu • • CACA • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • • • EkstremitasEkstremitas • • 100 x/mnt100 x/mnt • • 24 x/mnt24 x/mnt • • 35,535,5 °°CC • • +/++/+ • • +/++/+ •
• Atropi papil lidahAtropi papil lidah •
• SimetrisSimetris •
• VVesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) •
• BJ I II reguler, murmur (-), gallop (-)BJ I II reguler, murmur (-), gallop (-) •
• Cembung, asites (+), lien teraba diCembung, asites (+), lien teraba di
schuffner 2, hepar tidak teraba. schuffner 2, hepar tidak teraba.
•
• Edema ekstremitas (-)Edema ekstremitas (-) •
• Kuku sendok (+)Kuku sendok (+)
TANGGAL
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Cancel Anytime. • • SISI • • lidahlidah • • DadaDada • • ParuParu • • JantungJantung • • AbdomenAbdomen • • EkstremitasEkstremitas +/+ +/+
Atropi papil lidah Atropi papil lidah Simetris
Simetris V
Vesikuler (+/+), rhonki (-esikuler (+/+), rhonki (-/-), wheezing (-/-)/-), wheezing (-/-) BJ I II reguler, murmur (-), gallop (-)
BJ I II reguler, murmur (-), gallop (-)
Cembung, asites (+), lien teraba di schuffner 2, Cembung, asites (+), lien teraba di schuffner 2, hepar tidak teraba.
hepar tidak teraba. Edema ekstremitas (-) Edema ekstremitas (-) Kuku sendok (+) Kuku sendok (+)
TANGGAL
TANGGAL 31 Agustus 201231 Agustus 2012
Keluhan:
Keluhan: •• Sesak nafas (-)Sesak nafas (-) •
• Batuk berdahak (+)Batuk berdahak (+)
Pemeriksaan Fisik Pemeriksaan Fisik Kesadaran Kesadaran Keadaan Umum Keadaan Umum
Vital SignVital Sign
•
• Compos mentisCompos mentis •
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2
2.. ApApakakah ah didiagagnonosisis ps padada ka kasasuus is ini ni susuddah ah tetepapat?t? Di
Diagagnnoosisis s ppadada a kkasasuus s inini i susudadah h tetepapat t beberdrdasasararkkan an ananamamnenesisis,s, pemeriksaan fisik
pemeriksaan fisik dan pemeriksaan dan pemeriksaan penunjang yang telah penunjang yang telah dilakukan. Daridilakukan. Dari anamnesis diketahui bahwa pasien pernah mengkonsumsi alkohol dalam anamnesis diketahui bahwa pasien pernah mengkonsumsi alkohol dalam waktu lama, mengalami muntah darah (hematemesis) dan BAB hitam waktu lama, mengalami muntah darah (hematemesis) dan BAB hitam (melen
(melena), a), perut teraperut terasa kembunsa kembung dan semakin lamg dan semakin lama semakin mema semakin membesar besar (a
(asciscitetes) s) sehsehiningggga a terterasa asa sessesakak. . PaPada da pempemerieriksksaaaan n fifisik sik dididadapatpatkakann pembesaran lien (splenomegali),
pembesaran lien (splenomegali), penumpukan cairan di rongga peritonealpenumpukan cairan di rongga peritoneal (ascites), konjungtiva anemis, sclera ikterik. Pada pemeriksaan penunjang (ascites), konjungtiva anemis, sclera ikterik. Pada pemeriksaan penunjang di
ditemtemukukan an pepenunururunanan n alalbubumimin, n, USUSG G ababdodomemen n yayang ng memenununjnjukukkakann karakteristik sirosis hepatis.
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teratur dan terjadi penambahan jaringan ikat (fibrosis) di sekitar parenkim hati teratur dan terjadi penambahan jaringan ikat (fibrosis) di sekitar parenkim hati yang mengalami regenerasi.
yang mengalami regenerasi.
Insidens Insidens Pe
Pendndereritita a sisirorosisis s hahati ti lelebibih h babanynyak ak didijujumpmpai ai papada da kakaum um lalakiki-l-lakaki i jijikaka dibandingkan dengan kaum wanita sekita 1,6 : 1 dengan umur rata-rata terbanyak dibandingkan dengan kaum wanita sekita 1,6 : 1 dengan umur rata-rata terbanyak antara golongan umur 30 – 59 ta
antara golongan umur 30 – 59 tahun dengan puncaknya sekitar 40 – hun dengan puncaknya sekitar 40 – 449 tahun.449 tahun.
Klasifikasi Klasifikasi
Berdasarkan morfologi Sherlock membagi Sirosis hati atas 3 jenis, yaitu : Berdasarkan morfologi Sherlock membagi Sirosis hati atas 3 jenis, yaitu : 1
1.. MMiikkrroonnoodduullaar r 2
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4
4.. GlGlikikoononosisis s tytyppe-e-IVIV 5
5.. GGaallaakkttoosseemmiiaa 6
6.. TTiirroossiinneemmiiaa 7
7.. KKoolleessttaassiiss
Saluran empedu membawa empedu yang dihasilkan oleh hati ke usus, dimana Saluran empedu membawa empedu yang dihasilkan oleh hati ke usus, dimana empedu membantu mencerna lemak. Pada bayi penyebab sirosis terbanyak empedu membantu mencerna lemak. Pada bayi penyebab sirosis terbanyak adalah akibat tersumbatnya saluran empedu yang disebut Biliary atresia. Pada adalah akibat tersumbatnya saluran empedu yang disebut Biliary atresia. Pada penyakit
penyakit ini ini empedumemenuhi empedumemenuhi hati hati karena karena saluran saluran empedu empedu tidak tidak berfungsiberfungsi atau
atau rusrusak. ak. BayBayi i yanyang g menmenderiderita ta BilBiliary iary berberwarnwarna a kunkuning ing (ku(kulit lit kunkuninging)) setelah berusia satu bulan. Kadang bisa diatasi dengan pembedahan untuk setelah berusia satu bulan. Kadang bisa diatasi dengan pembedahan untuk membentuk saluran baru agar empedu meninggalkan hati, tetapi transplantasi membentuk saluran baru agar empedu meninggalkan hati, tetapi transplantasi diindikasikan untuk anak-anak yang menderita penyakit hati stadium akhir. diindikasikan untuk anak-anak yang menderita penyakit hati stadium akhir.
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3
3.. AAssiitteess 4.
4. EnEnsesefafalolophphatati hi hepepatatititisis
Keluhan dari sirosis hati dapat berupa : Keluhan dari sirosis hati dapat berupa : a.
a. MerMerasa asa kekemamampmpuauan jn jasmasmanani mi menenururunun b.
b. Nausea, nafsu makan menurun dan diikuti dengNausea, nafsu makan menurun dan diikuti dengan penurunan berat badanan penurunan berat badan c.
c. Mata Mata berberwarnwarna kua kuninning dag dan bn buanuang aig air ker kecil bcil berwerwarnarna gea gelaplap d.
d. PemPembebesarsaran pan peruerut dat dan kn kakaki bi benengkgkak ak e.
e. PePerdrdararahaahan sn salalururan an cercerna na babagigian an atatasas aa
aaPadPada a keakeadaan daan lanlanjut jut dapdapat at dijdijumpumpai ai pasipasien en tidtidak ak sadasadarkarkan n dirdiri i (He(Hepatpaticic Enchephalopathy)
Enchephalopathy) g.
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b.
b. spleenomegalispleenomegali aa
aa perubahan sumsum tulang perubahan sumsum tulang aa
aa caput medusacaput medusa ee.. aassiitteess
ff.. ccoollllaatteerraal l vveeiinnhheemmoorrrrhhooiidd g
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Penatalaksanaan Penatalaksanaan
Pengobatan sirosis hati pada prinsipnya berupa : Pengobatan sirosis hati pada prinsipnya berupa : 1
1.. SSiimmttoommaattiiss 2
2.. SuSupppporortitif, f, yyaiaitu tu :: a.
a. IstiIstirahrahat yat yang ang cukcukupup aa
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Pemberian diuretic hanya bagi penderita yang telah menjalani diet rendah Pemberian diuretic hanya bagi penderita yang telah menjalani diet rendah garam dan pembatasan cairan namun penurunan berat badannya kurang garam dan pembatasan cairan namun penurunan berat badannya kurang dari 1 kg setelah 4 hari. Mengingat salah satu komplikasi akibat pemberian dari 1 kg setelah 4 hari. Mengingat salah satu komplikasi akibat pemberian diuretic adala hipokalemia dan hal ini dapat mencetuskan encepalophaty diuretic adala hipokalemia dan hal ini dapat mencetuskan encepalophaty hepatic, maka pilihan utama diuretic adalah spironolacton, dan dimulai hepatic, maka pilihan utama diuretic adalah spironolacton, dan dimulai dengan dosis rendah, serta dapat dinaikkan dosisnya bertahap tiap 3-4 hari, dengan dosis rendah, serta dapat dinaikkan dosisnya bertahap tiap 3-4 hari,
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o
o Start antibiotic if ascites > 250 mm polymorphsStart antibiotic if ascites > 250 mm polymorphs
o
o 50% die50% die
o
o 69 % recure in 1 year 69 % recure in 1 year
Pe
Pengngobobataatan n SBSBP P dedengngan an memembmberierikakan n CeCephphaloalosposporirins ns GeGenenerasrasi i IIIIII (Cefotaxime), secara parental selama lima hari, atau Qinolon secara oral. (Cefotaxime), secara parental selama lima hari, atau Qinolon secara oral. Mengi
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pasien
pasien yang yang akan akan dilakukan dilakukan transplantasi. transplantasi. Pilihan Pilihan terbaik terbaik adalahadalah transplantasi hati yang diikuti dengan perbaikan dan fungsi ginjal.
transplantasi hati yang diikuti dengan perbaikan dan fungsi ginjal.
Ensefalophaty hepatic Ensefalophaty hepatic
Suatu sindrom neuropsikiatri yang didapatkan pada penderita penyakit hati Suatu sindrom neuropsikiatri yang didapatkan pada penderita penyakit hati menahun, mulai dari gangguan ritme tidur, perubahan kepribadian, gelisah menahun, mulai dari gangguan ritme tidur, perubahan kepribadian, gelisah
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