REFERAT
REFERAT
KATARAK KONGENITAL
KATARAK KONGENITAL
Oleh:
Oleh:
Eka Aprillia Arum Kanti
Eka Aprillia Arum Kanti
0818011017
0818011017
Pembimbing:
Pembimbing:
dr. Junita Shara Sp.M
dr. Junita Shara Sp.M
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Katarak adalah perubahan lensa mata yang
Katarak adalah perubahan lensa mata yang
sebelumnya jernih dan tembus cahaya menjadi
sebelumnya jernih dan tembus cahaya menjadi
keruh
keruh
Dimana tidak bisa melihat dengan jelas karena
Dimana tidak bisa melihat dengan jelas karena
dengan lensa yang keruh cahaya sulit mencapai
dengan lensa yang keruh cahaya sulit mencapai
retina dan akan menghasilkan bayangan yang
retina dan akan menghasilkan bayangan yang
kabur pada retina.
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Katarak kongenital
Katarak kongenital
adalah katarak yang
adalah katarak yang
mulai terjadi sebelum atau segera
mulai terjadi sebelum atau segera setelah
setelah
kela
kelahiran dan bayi
hiran dan bayi yang berusia kurang dari
yang berusia kurang dari
satu tahun, dapat timbul pada satu atau
satu tahun, dapat timbul pada satu atau
kedua mata
kedua mata
Sebuah katarak disebut kongenital bila ada
Sebuah katarak disebut kongenital bila ada
saat lahir
saat lahir
Dikenal
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Etiologi
Etiologi
Herediter (isolated
Herediter (isolated
–
–
tanpa dihubungkan
tanpa dihubungkan
dengan kelai
dengan kelainan mata
nan mata atau sistemik)
atau sistemik)
Herediter yang dihubungkan dengan kelainan
Herediter yang dihubungkan dengan kelainan
sistemik dan sindrom multisistem
sistemik dan sindrom multisistem
Infeksi
Infeksi
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Klasifikasi
Klasifikasi
Katarak Lamellar atau Zonular
Katarak Lamellar atau Zonular
- Umumya diturunkan secara genetik
- Umumya diturunkan secara genetik
- Secara klinis tampak sebagai lapisan yang keruh yang
- Secara klinis tampak sebagai lapisan yang keruh yang
mengelilingi daerah yang jernih
mengelilingi daerah yang jernih
dan dikelilingi korteks yang
dan dikelilingi korteks yang
jernih juga
jernih juga
Katarak Polar
Katarak Polar
- Kekeruhan lensa yang meliputi korteks subkapsular dan
- Kekeruhan lensa yang meliputi korteks subkapsular dan
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Katarak Sutural / Stellate
Katarak Sutural / Stellate
- Kekeruhan pada bentuk
- Kekeruhan pada bentuk
Y-sutures
Y-sutures
atau
atau
inverted-Y
inverted-Y
pada
pada
nukleus fetal
nukleus fetal
- Biasanya tidak
- Biasanya tidak
menyebabkan gangguan penglihatan
menyebabkan gangguan penglihatan
Katarak Coronary
Katarak Coronary
--
Terdiri dari sekelompok
Terdiri dari sekelompok
club-shaped opacities
club-shaped opacities
pada korteks
pada korteks
yang tersusun disekitar ekuator lensa seperti mahkota atau
yang tersusun disekitar ekuator lensa seperti mahkota atau
korona
korona
- terlihat saat pupil dilatasi dan biasanya tidak
- terlihat saat pupil dilatasi dan biasanya tidak
mempengaruhi ketajaman penglihatan
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Katarak Nuklear
Katarak Nuklear
- Kekeruhan dapat hanya terjadi pada nukleus embrional saja
- Kekeruhan dapat hanya terjadi pada nukleus embrional saja
atau pada nukelus embrional dan
atau pada nukelus embrional dan fetal nuclei
fetal nuclei
--
Biasanya bersifat bilateral dengan spektrum tingkat
Biasanya bersifat bilateral dengan spektrum tingkat
keparahan yang luas
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Katarak Membranosa
Katarak Membranosa
- Dimana terjadi absorbsi protein lensa yang utuh
- Dimana terjadi absorbsi protein lensa yang utuh
maupun tidak, menyebabkan kapsul anterior dan
maupun tidak, menyebabkan kapsul anterior dan
posterior menyatu menjadi
posterior menyatu menjadi
dense white membrane
dense white membrane
-Menimbulkan
gangguan
penglihatan
yang
-Menimbulkan
gangguan
penglihatan
yang
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Diagnosis
Diagnosis
Seharusnya dilakukan pemeriksaan mata pada
Seharusnya dilakukan pemeriksaan mata pada
seluruh bayi baru lahir sebagai skrinning, yaitu :
seluruh bayi baru lahir sebagai skrinning, yaitu :
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Anamnesa
Anamnesa
Diperlukan anamnesa yang detail tentang hambatan tumbuh kembang
Diperlukan anamnesa yang detail tentang hambatan tumbuh kembang
anak, pola makan anak, lesi-lesi kulit, kelainan-kelainan perkembangan
anak, pola makan anak, lesi-lesi kulit, kelainan-kelainan perkembangan
yang lain serta riwayat keluarga di dalam mendiagnosa katarak
yang lain serta riwayat keluarga di dalam mendiagnosa katarak
kongenital
kongenital
Fungsi V
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Diagnosis Banding
Diagnosis Banding
Retin
Retinoblastoma (11% unilateral
oblastoma (11% unilateral dan 7%
dan 7%
bilateral)
bilateral)
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