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PPT KATARAK KONGENITAL

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REFERAT

REFERAT

KATARAK KONGENITAL

KATARAK KONGENITAL

Oleh:

Oleh:

Eka Aprillia Arum Kanti

Eka Aprillia Arum Kanti

0818011017

0818011017

Pembimbing:

Pembimbing:

dr. Junita Shara Sp.M

dr. Junita Shara Sp.M

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Katarak adalah perubahan lensa mata yang

Katarak adalah perubahan lensa mata yang

sebelumnya jernih dan tembus cahaya menjadi

sebelumnya jernih dan tembus cahaya menjadi

keruh

keruh

Dimana tidak bisa melihat dengan jelas karena

Dimana tidak bisa melihat dengan jelas karena

dengan lensa yang keruh cahaya sulit mencapai

dengan lensa yang keruh cahaya sulit mencapai

retina dan akan menghasilkan bayangan yang

retina dan akan menghasilkan bayangan yang

kabur pada retina.

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Katarak kongenital

Katarak kongenital

 adalah katarak yang

 adalah katarak yang

mulai terjadi sebelum atau segera

mulai terjadi sebelum atau segera setelah

setelah

kela

kelahiran dan bayi

hiran dan bayi yang berusia kurang dari

yang berusia kurang dari

satu tahun, dapat timbul pada satu atau

satu tahun, dapat timbul pada satu atau

kedua mata

kedua mata

Sebuah katarak disebut kongenital bila ada

Sebuah katarak disebut kongenital bila ada

saat lahir

saat lahir

Dikenal

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Etiologi

Etiologi

Herediter (isolated

Herediter (isolated

 tanpa dihubungkan

 tanpa dihubungkan

dengan kelai

dengan kelainan mata

nan mata atau sistemik)

atau sistemik)

Herediter yang dihubungkan dengan kelainan

Herediter yang dihubungkan dengan kelainan

sistemik dan sindrom multisistem

sistemik dan sindrom multisistem

Infeksi

Infeksi

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Klasifikasi

Klasifikasi

Katarak Lamellar atau Zonular

Katarak Lamellar atau Zonular

- Umumya diturunkan secara genetik

- Umumya diturunkan secara genetik

- Secara klinis tampak sebagai lapisan yang keruh yang

- Secara klinis tampak sebagai lapisan yang keruh yang

mengelilingi daerah yang jernih

mengelilingi daerah yang jernih

dan dikelilingi korteks yang

dan dikelilingi korteks yang

 jernih juga

 jernih juga

Katarak Polar

Katarak Polar

- Kekeruhan lensa yang meliputi korteks subkapsular dan

- Kekeruhan lensa yang meliputi korteks subkapsular dan

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Katarak Sutural / Stellate

Katarak Sutural / Stellate

- Kekeruhan pada bentuk

- Kekeruhan pada bentuk

Y-sutures

Y-sutures

atau

atau

inverted-Y

inverted-Y

pada

pada

nukleus fetal

nukleus fetal

- Biasanya tidak

- Biasanya tidak

menyebabkan gangguan penglihatan

menyebabkan gangguan penglihatan

Katarak Coronary

Katarak Coronary

--

Terdiri dari sekelompok

Terdiri dari sekelompok

club-shaped opacities

club-shaped opacities

pada korteks

pada korteks

yang tersusun disekitar ekuator lensa seperti mahkota atau

yang tersusun disekitar ekuator lensa seperti mahkota atau

korona

korona

- terlihat saat pupil dilatasi dan biasanya tidak

- terlihat saat pupil dilatasi dan biasanya tidak

mempengaruhi ketajaman penglihatan

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Katarak Nuklear

Katarak Nuklear

- Kekeruhan dapat hanya terjadi pada nukleus embrional saja

- Kekeruhan dapat hanya terjadi pada nukleus embrional saja

atau pada nukelus embrional dan

atau pada nukelus embrional dan fetal nuclei

 fetal nuclei

--

Biasanya bersifat bilateral dengan spektrum tingkat

Biasanya bersifat bilateral dengan spektrum tingkat

keparahan yang luas

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Katarak Membranosa

Katarak Membranosa

- Dimana terjadi absorbsi protein lensa yang utuh

- Dimana terjadi absorbsi protein lensa yang utuh

maupun tidak, menyebabkan kapsul anterior dan

maupun tidak, menyebabkan kapsul anterior dan

posterior menyatu menjadi

posterior menyatu menjadi

dense white membrane

dense white membrane

-Menimbulkan

gangguan

penglihatan

yang

-Menimbulkan

gangguan

penglihatan

yang

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Diagnosis

Diagnosis

Seharusnya dilakukan pemeriksaan mata pada

Seharusnya dilakukan pemeriksaan mata pada

seluruh bayi baru lahir sebagai skrinning, yaitu :

seluruh bayi baru lahir sebagai skrinning, yaitu :

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Anamnesa

Anamnesa

Diperlukan anamnesa yang detail tentang hambatan tumbuh kembang

Diperlukan anamnesa yang detail tentang hambatan tumbuh kembang

anak, pola makan anak, lesi-lesi kulit, kelainan-kelainan perkembangan

anak, pola makan anak, lesi-lesi kulit, kelainan-kelainan perkembangan

yang lain serta riwayat keluarga di dalam mendiagnosa katarak

yang lain serta riwayat keluarga di dalam mendiagnosa katarak

kongenital

kongenital

Fungsi V

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Diagnosis Banding

Diagnosis Banding

Retin

Retinoblastoma (11% unilateral

oblastoma (11% unilateral dan 7%

dan 7%

bilateral)

bilateral)

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