Challenges of Living with Cystic Fibrosis-Questionnaire
Assessing the impact of administering the 'Challenges of Living with Cystic Fibrosis' questionnaire on the self-efficacy of caregivers of children with cystic fibrosis
... these challenges to family life can lead to increased amounts stress for the ...threats, challenges and competence all influence the coping strategies they adapt to deal with various ...
154
Assessing the responsiveness of the "Challenge of Living with Cystic Fibrosis" questionnaire to change in clinical condition
... the questionnaire could never have been developed; furthermore, thanks to Alder Hey’s Charitable Funds Department for the generous bursary enabling me to pay my tuition fees and eat for the past ...
139
Living with cystic fibrosis – a qualitative study of a life coaching intervention
... According to Bohart and Tallman, 33,34 people actively make changes when they are ready, but the change process is best supported when a person feels understood, accepted, and listened to. A systematic review conducted ...
10
Gene therapy for cystic fibrosis: challenges and future directions
... A survey of human lung tissues revealed essentially no a/v, protein in differentiated cells of nasal and proximal airway epithelia, consistent with the difficulties in achieving gene tra[r] ...
9
Prescribing practices for intravenous aminoglycosides in UK cystic fibrosis clinics: a questionnaire survey
... ABSTRACT Background: Intravenous aminoglycoside antibiotics are widely used to treat pulmonary infection with Pseudomonas aeruginosa in individuals with cystic fibrosis (CF). Over the last decade evidence ...
10
Nutrition in cystic fibrosis
... in Cystic fibrosis patients has significantly increased in recent ...individuals living with cystic fibrosis remain, according to different international registries, under proposed ...
7
An Overview on Cystic Fibrosis
... people living with cystic fibrosis in the UK and 1 in 25 of the population is a carrier of the cystic fibrosis gene ...with cystic fibrosis in 2000 will be _50 ...
12
Cystic Fibrosis: A Review
... CONCLUSION Cystic fibrosis remains a life-shortening condition associated with significant morbidity, recent advances and new treatments offer great hope and ...are living with more mild disease and ...
7
Challenges in Cystic Fibrosis Newborn Screening and Recommendations for Primary Care Physicians
... applied cystic fi brosis transmembrane conductance regulator gene ( CFTR ) sequencing for the fi rst time, required detection of 2 mutations for designation of positive screening, and recommendation of a sweat ...
6
Living a ‘normal life’? Formal and informal supports in the lives of adults with cystic fibrosis
... independent living promoted by the UK disabled people’s movement, the adults with CF in this sample tended not to see themselves as disabled and had little exposure to UK disability ...
13
Living with cystic fibrosis : a phenomenological study of children, adolescents, young adults and their parents
... investigates the experience of children and their parents who live with a chronic, life- threatening and life-limiting disease - cystic fibrosis (CF).. Affected families must follow a r[r] ...
356
European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre
... 12. Challenges relating to developing health services in low income countries The aim of the ECFS Standards of Care Guidelines is to improve the quality of care for patients with CF and to establish best practice ...
20
Clinical Practice Guidelines From the Cystic Fibrosis Foundation for Preschoolers With Cystic Fibrosis
... Cystic fibrosis (CF) clinical care guidelines exist for the care of infants up to age 2 years and for individuals ≥ 6 years of ...Several challenges exist that may impede the delivery of care for ...
28
Exercise capacity in patients with cystic fibrosis vs. non-cystic fibrosis bronchiectasis.
... Age, sex, height, body mass, body mass index (BMI) as well as z-scores for body mass index (BMI) based on Center of disease and control (CDC) criteria. Etiology of bronchiectasis, chest CT and echocardiography were ...
12
US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non tuberculous mycobacteria in individuals with cystic fibrosis
... Acquisition of NTM through cross-infection Person-to-person transmission of NTM has traditionally been considered unlikely. Two separate studies have shown that patients, even siblings living in the same household ...
23
The Pulmonary Microbiome in Cystic Fibrosis
... with cystic fibrosis ...of cystic fibrosis transmembrane conductance regulator (CFTR) ...many challenges that must be overcome if microbiome profiling is going to influence future ...
22
Lung Transplantation and Cystic Fibrosis
... about living with this severe and potentially fatal genetic ...with cystic fibrosis can discuss the treatments, programs and services available in their province/region, via video chat and instant ...
11
Cystic fibrosis is the result of a defect in the cystic fibrosis
... Management Pancreatic Enzyme Replacement Therapy The pancreas is responsible for secreting enzymes that aid in the absorption of nutrients, including fat-soluble vitamins (vitamins A, D, E, and K). In order to counteract ...
5
Cystic fibrosis
... Thus, the sweat gland shows two abnormalities in CF: in the duct, decreased Cl- transport inhibits fluid absorption; in the secretory coil, decreased Cl- transport inhibits cAMP-me- diat[r] ...
5