Alveolar proteinosis
Whole lung lavage combined with Granulocyte-macrophage colony stimulating factor inhalation for an adult case of refractory pulmonary alveolar proteinosis
... Pulmonary alveolar proteinosis (PAP) is a rare but treat- able disease that is characterized by the accumulation of a periodic acid Schiff (PAS) positive lipoproteinaceous substance in the ...pulmonary ...
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Pulmonary Alveolar Proteinosis: A Comprehensive Clinical Perspective
... the alveolar airspaces can be filled with various materials, which frequently replace the air necessary for gas exchange and give rise to alveolar filling syndromes (Table ...Pulmonary alveolar ...
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Impaired lipid metabolism in idiopathic pulmonary alveolar proteinosis
... Pulmonary alveolar proteinosis (PAP) is a rare lung dis- ease in which the alveolar spaces are filled with lipopro- teinaceous material [1,2]. PAP occurs in three clinically distinct forms: ...
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Pulmonary alveolar proteinosis and first successful whole lung lavage in Sri Lanka: a case report
... pulmonary alveolar proteinosis. An open lung biopsy revealed intra-alveolar granular amphophilic material which was strongly periodic acid – Schiff positive and diastase resistant, which is ...
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Pulmonary alveolar proteinosis: diagnostic and therapeutic challenges
... Pulmonary Alveolar Proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces. It occurs with a reported prevalence of 0.1 per 100,000 ...
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Long-term follow-up and treatment of congenital alveolar proteinosis
... Case presentation: A 2 1/2 years old girl was diagnosed as having alveolar proteinosis. Whole lung lavages were performed with a new catheter balloon technique, feasible in small sized airways. Because of ...
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Pulmonary Alveolar Proteinosis: Experience With Eight Pediatric Cases and a Review
... Partial and massive lung lavages in an infant with severe pulmonary alveolar proteinosis. Seard C, Wasserman K, Benfield JR[r] ...
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Case Report A noninvasive examination for the diagnosis of pulmonary alveolar proteinosis: induced sputum in conjunction with transmission electron microscopy
... Pulmonary alveolar proteinosis (PAP), first described in 1958, is a rare diffuse lung dis- ease characterized by the accumulation of peri- odic acid Schiff (PAS)-positive surfactant-asso- ciated ...
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Rituximab for auto-immune alveolar proteinosis, a real life cohort study
... Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by deposition of extracellular lipoprotei- naceous material within pulmonary alveoli ...by alveolar macrophages [2 – ...8]. ...
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Elderly-onset hereditary pulmonary alveolar proteinosis and its cytokine profile
... Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterized by the accumulation of surfactant proteins, which causes progressive respiratory insuffi- ciency ...by alveolar macrophages ...
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Assessment and management of pulmonary alveolar proteinosis in a reference center
... Pulmonary alveolar proteinosis (PAP) is a syndrome characterized by the accumulation of surfactant within alveolar macrophages and alveoli, which impairs pul- monary gas transfer and results in ...
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Elemental analysis of lung tissue particles and intracellular iron content of alveolar macrophages in pulmonary alveolar proteinosis
... Pulmonary alveolar proteinosis (PAP) is a rare disease occurred by idiopathic (autoimmune) or secondary to particle ...inside alveolar macrophages was stained with Berlin blue, and its distribution ...
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Rituximab therapy in pulmonary alveolar proteinosis improves alveolar macrophage lipid homeostasis
... Pulmonary Alveolar Proteinosis (PAP) patients exhibit an acquired deficiency of biologically active granulocyte-macrophage colony stimulating factor (GM-CSF) attributable to GM-CSF specific ...PAP ...
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Clinical significance of serum lipids in idiopathic pulmonary alveolar proteinosis
... Pulmonary alveolar proteinosis(PAP) is a rare disease characterized by the accumulation of lipoproteinaceous material in the ...the alveolar spaces of the lungs with the lipoproteinaceous material ...
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Pulmonary Alveolar Proteinosis: A Comprehensive Clinical Perspective
... the alveolar airspaces can be filled with various materials, which frequently replace the air necessary for gas exchange and give rise to alveolar filling syndromes (Table ...Pulmonary alveolar ...
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Unsuspected pulmonary alveolar proteinosis in a patient with acquired immunodeficiency syndrome: a case report
... Case presentation: A 42-year-old African American man infected with human immunodeficiency virus was admitted with chronic respiratory symptoms and diffuse pulmonary infiltrates. Chest computed tomography revealed ...
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Characterization of CSF2RA mutation related juvenile pulmonary alveolar proteinosis
... The Kids Lung Register database [18] was screened for pediatric patients with pulmonary alveolar proteinosis aged 0–18 years (n = 9). All patients had been classified by ex- perienced clinicians from 6 ...
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Pulmonary alveolar proteinosis
... ulmonary alveolar proteinosis (PAP) is a rare disease characterised by alveolar accumulation of surfactant composed of proteins and lipids due to defective surfactant clearance by alveolar ...
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Serum KL-6 is a predictor of outcome in pulmonary alveolar proteinosis
... A-aDO2: Alveolar arterial oxygen gradient; BALF: Bronchoalveolar lavage fluid; CTD: Connective tissue disease; DLCO: Diffusing capacity of the lung for carbon monoxide; ELISA: Enzyme-linked immunosorbent assay; ...
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The parallel lives of alpha1-antitrypsin deficiency and pulmonary alveolar proteinosis
... In 1963, five cases of alpha1-antitrypsin deficiency were reported in the scientific literature, as well as an attempt to treat pulmonary alveolar proteinosis by a massive washing of the lung (whole lung ...
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