Chronic granulomatous
Continuous Antibiotic Therapy in Chronic Granulomatous Disease: Preliminary Communication
... Continuous Antibiotic Therapy in Chronic Granulomatous Disease: Preliminary. Services[r] ...
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Corticosteroids in the Management of Cystitis Secondary to Chronic Granulomatous Disease
... Gastric outlet obstruction in chronic granulomatous disease of childhood. Kontras SB, Bodenbander JG, McClave CR, et al[r] ...
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Host defense molecule polymorphisms influence the risk for immune mediated complications in chronic granulomatous disease
... Chronic granulomatous disease (CGD) is an inherited dis- order of phagocyte function in which defective superoxide production results in deficient microbicidal ...develop chronic gastrointestinal ...
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Chronic granulomatous disease: a review of the infectious and inflammatory complications
... include chronic granulomatous disease (CGD), neutrophil adhe- sion defects (such as the leukocyte adhesion deficiency syndromes), Chediak-Higashi syndrome, Griscelli syn- drome, Kostmann’s syndrome, WHIM ...
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Citation classics in chronic granulomatous disease: a bibliometric analysis
... Abstract: The number of times a scientific article has been cited reflects its impact on a specific field. Highly cited articles are known as citation classics. Here, we aim to characterize the most frequently cited ...
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X linked Inheritance in Females with Chronic Granulomatous Disease
... Chronic granulomatous disease in males is familial and its transmission is is usually clearly ...with chronic granulomatous disease had extremely low chemiluminescence production, their ...
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Gastric Antral Narrowing in Chronic Granulomatous Disease of Childhood
... When those diagnoses are being considered because of an antral abnormality shown by roentgenograms or uncertain findings from a gastric biopsy, an NBT test for chronic granulomatous dise[r] ...
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CHRONIC GRANULOMATOUS DISEASE: CORRELATION BETWEEN PATHOGENESIS AND CLINICAL FINDINGS
... drogen peroxide antibacterial system. : Quantita- tive nitroblue tetrazoliiiii, test in chronic granuloniatous disease. A.: Chronic granulomatous disease in females: A deficiency of leuk[r] ...
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Preliminary study on chronic granulomatous disease in Sri Lanka
... Keywords: Chronic granulomatous disease, NADPH oxidase, CYBB, NCF1, Mycobacterial infections, X-linked, Autosomal recessive, Sri Lanka.. © The Author(s) 2018.[r] ...
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Therapeutic effects of proteoliposomes on X-linked chronic granulomatous disease: proof of concept using macrophages differentiated from patient-specific induced pluripotent stem cells
... Keywords: protein therapy, proteoliposomes, chronic granulomatous disease, NADPH oxidase, induced pluripotent stem cells, macrophages.. Introduction.[r] ...
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Recombinant interferon gamma augments phagocyte superoxide production and X chronic granulomatous disease gene expression in X linked variant chronic granulomatous disease
... of chronic granulomatous disease (CGD) by studying its effects on CGD phagocyte superoxide generation, NADPH oxidase kinetics, cytochrome b559 content, and expression of X-CGD (the gene for the X-linked ...
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Chronic Granulomatous Disease Presenting as Hemophagocytic Lymphohistiocytosis: A Case Report
... Chronic granulomatous disease (CGD) is a primary immunode fi ciency characterized by recurrent infections and a dysregulated in fl ammatory response. Infection-triggered hemophagocytic lymphohistiocytosis ...
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NADPH oxidase deficiency in X linked chronic granulomatous disease
... deficiency of myeloperoxidase, and 7 patients with X-linked chronic granulomatous disease (CGD). When measured under optimal conditions (at pH 5.5 and in the presence of 0.5 mM Mn++), NADPH oxidase activity ...
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Correction of metabolic deficiencies in the leukocytes of patients with chronic granulomatous disease
... with chronic granulomatous disease (CGD) exhibit metabolic and bactericidal deficiencies that may be the result of inadequate production of H 2 O 2 ...
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Cytochrome b deficiency in an autosomal form of chronic granulomatous disease A third form of chronic granulomatous disease recognized by monocyte hybridization
... autosomal because the granulocytes of both parents (first cousins) and a nonaffected sister of the patients expressed 70-80% of the normal cytochrome b signal, showed low-normal or subnormal oxidative reactions during ...
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Disseminated BCG in Twin Boys with Presumed Chronic Granulomatous Disease of Childhood
... Disseminated BCG in Twin Boys with Presumed Chronic Granulomatous Disease of. http://pediatrics.aappublications.org/content/48/1/141[r] ...
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Nocardia farcinica Pneumonia in Chronic Granulomatous Disease
... with chronic granulomatous dis- ease (CGD) because the signs and symptoms are often nonspecific, delay in diagnosis is common, and invasive procedures are frequently required to obtain appropriate tissue ...
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Chronic Recurrent Multifocal Osteomyelitis and Thalidomide in Chronic Granulomatous Disease
... Chronic granulomatous disease (CGD) is an uncommon primary immune deficiency caused by abnormal phagocytic activity. The disease results from defects of dinucleotide phosphate oxidase (NADPH oxidase), an ...
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Gastrointestinal Involvement in Chronic Granulomatous Disease
... Conclusion. GI involvement is a common and recur- ring problem in CGD, especially in those with X-linked inheritance. Currently, there is no clear evidence for an infectious cause. The frequency of GI involvement is ...
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Sarcoidosis in Chronic Granulomatous Disease
... In addition to increased susceptibility to infections in patients with chronic granulomatous disease (CGD), a higher incidence of sterile inflammatory disorders in these patients has been noted. However, ...
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