chronic granulomatous disease
Continuous Antibiotic Therapy in Chronic Granulomatous Disease: Preliminary Communication
... Continuous Antibiotic Therapy in Chronic Granulomatous Disease: Preliminary. Services[r] ...
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NADPH oxidase deficiency in X linked chronic granulomatous disease
... deficiency of myeloperoxidase, and 7 patients with X-linked chronic granulomatous disease (CGD). When measured under optimal conditions (at pH 5.5 and in the presence of 0.5 mM Mn++), NADPH oxidase ...
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Host defense molecule polymorphisms influence the risk for immune mediated complications in chronic granulomatous disease
... Chronic granulomatous disease (CGD) is an inherited dis- order of phagocyte function in which defective superoxide production results in deficient microbicidal ...develop chronic ...
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Citation classics in chronic granulomatous disease: a bibliometric analysis
... Abstract: The number of times a scientific article has been cited reflects its impact on a specific field. Highly cited articles are known as citation classics. Here, we aim to characterize the most frequently cited ...
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Disseminated BCG in Twin Boys with Presumed Chronic Granulomatous Disease of Childhood
... Disseminated BCG in Twin Boys with Presumed Chronic Granulomatous Disease of. http://pediatrics.aappublications.org/content/48/1/141[r] ...
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X linked Inheritance in Females with Chronic Granulomatous Disease
... Chronic granulomatous disease in males is familial and its transmission is is usually clearly ...this disease is associated with an absence of the respiratory burst generated in stimulated ...
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Corticosteroids in the Management of Cystitis Secondary to Chronic Granulomatous Disease
... Gastric outlet obstruction in chronic granulomatous disease of childhood. Kontras SB, Bodenbander JG, McClave CR, et al[r] ...
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Cytochrome b deficiency in an autosomal form of chronic granulomatous disease A third form of chronic granulomatous disease recognized by monocyte hybridization
... autosomal because the granulocytes of both parents (first cousins) and a nonaffected sister of the patients expressed 70-80% of the normal cytochrome b signal, showed low-normal or subnormal oxidative reactions during ...
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Chronic Recurrent Multifocal Osteomyelitis and Thalidomide in Chronic Granulomatous Disease
... Chronic granulomatous disease (CGD) is an uncommon primary immune deficiency caused by abnormal phagocytic ...The disease results from defects of dinucleotide phosphate oxidase (NADPH ...
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Therapeutic effects of proteoliposomes on X-linked chronic granulomatous disease: proof of concept using macrophages differentiated from patient-specific induced pluripotent stem cells
... Keywords: protein therapy, proteoliposomes, chronic granulomatous disease, NADPH oxidase, induced pluripotent stem cells, macrophages.. Introduction.[r] ...
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Chronic Granulomatous Disease Presenting as Hemophagocytic Lymphohistiocytosis: A Case Report
... Chronic granulomatous disease (CGD) is a primary immunode fi ciency characterized by recurrent infections and a dysregulated in fl ammatory response. Infection-triggered hemophagocytic ...
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Recombinant interferon gamma augments phagocyte superoxide production and X chronic granulomatous disease gene expression in X linked variant chronic granulomatous disease
... of chronic granulomatous disease (CGD) by studying its effects on CGD phagocyte superoxide generation, NADPH oxidase kinetics, cytochrome b559 content, and expression of X-CGD (the gene for the ...
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CHRONIC GRANULOMATOUS DISEASE: CORRELATION BETWEEN PATHOGENESIS AND CLINICAL FINDINGS
... drogen peroxide antibacterial system. : Quantita- tive nitroblue tetrazoliiiii, test in chronic granuloniatous disease. A.: Chronic granulomatous disease in females: A deficiency of leuk[r] ...
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Deficient flavoprotein component of the NADPH dependent O2 generating oxidase in the neutrophils from three male patients with chronic granulomatous disease
... chronic granulomatous disease patients had undetectable amounts of cytochrome b559 whereas the third patient had a normal content of cytochrome b559, which was spectrally indistinguishable from the ...
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Degranulation of leukocytes in chronic granulomatous disease
... Quantitative chemical analyses of the subcellular distribution patterns for acid and alkaline phosphatase, beta glucuronidase and peroxidase were obtained for human peripheral blood leukocytes of four patients with ...
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Staphylococci surviving intracellularly in phagocytes from patients suffering from chronic granulomatous disease are killed in vitro by antibiotics encapsulated in liposomes
... Granulocytes and monocytes/macrophages from patients suffering from chronic granulomatous disease (CGD) are ineffective in killing specific kinds of phagocytized bacteria, e.g., Staphylococcus ...
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Correction of metabolic deficiencies in the leukocytes of patients with chronic granulomatous disease
... with chronic granulomatous disease (CGD) exhibit metabolic and bactericidal deficiencies that may be the result of inadequate production of H 2 O 2 ...
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Recent Advances in Gene Therapy and Modeling of Chronic Granulomatous Disease
... The Chronic granulomatous disease (CGD) is a primary immunodeficiency that characterized by mutations in phagocyte nicotinamide adenine dinucleotide phosphate (NADPH) oxidase, resulting in deficient ...
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Gastric Antral Narrowing in Chronic Granulomatous Disease of Childhood
... When those diagnoses are being considered because of an antral abnormality shown by roentgenograms or uncertain findings from a gastric biopsy, an NBT test for chronic granulomatous dise[r] ...
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Chronic granulomatous disease: a review of the infectious and inflammatory complications
... dermatitis-like disease but with systemic or deep seated infections [131], facial granulomata [132] and discoid lupus, and seborrheic dermatitis-like disease ...and granulomatous of fungal skin ...
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