Connective Tissue Disease
Mixed connective tissue disease complicated by heart failure in Ile-Ife, Nigeria: management challenges in a resource-limited economy
... to connective tissue disease (CTD), with features of pulmonary arterial hyper- tension (PAH) as shown in Figure 2, but no pleural ...soft tissue swell- ing over the IP joints, complete ...
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Mixed Connective Tissue Disease in Children and Adolescents
... A review of 234 reported patients with mixed connective tissue disease, including 50 pediatric patients, suggests a higher prevalence of renal and cardiac disease in affected children an[r] ...
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Circulating 20S Proteasome Levels in Patients with Mixed Connective Tissue Disease and Systemic Lupus Erythematosus
... parallel disease activity ...ical disease indices and serologic parameters in patients with SLE is unknown, and c20S have not been studied in mixed connective tissue disease ...with ...
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Esophageal Motor Abnormalities in Children and Adolescents With Scleroderma and Mixed Connective Tissue Disease
... nective tissue disease, esophageal manometry was per- formed on seven patients with progressive systemic sclerosis, four patients with mixed connective tissue.. disease, and two patients[r] ...
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Connective tissue disease-associated pulmonary arterial hypertension.
... in connective tissue disease, with differential patterns of gas exchange on non-invasive exercise testing distinguishing pul- monary vascular disease from left heart disease in systemic ...
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Vitamin D deficiency in undifferentiated connective tissue disease
... winter periods (UCTD summer: 33 ± 13.4 ng/mL versus control: 39.9 ± 11.7 ng/mL, P = 0.01; UCTD winter: 27.8 ± 12.48 ng/ mL versus control: 37.8 ± 12.3 ng/mL, P = 0.0001). The presence of dermatological symptoms ...
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Mean pulmonary arterial pressure as a prognostic indicator in connective tissue disease associated with interstitial lung disease: a retrospective cohort study
... This study was approved by the Tosei General Hos- pital Institutional Review Board (IRB No. 483). Patient records and information were anonymized and de- identified prior to analysis. The diagnosis of ILD was made ...
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First report of cardiac tamponade in pediatric onset mixed connective tissue disease
... Mixed Connective Tissue Disease (MCTD) is a rare condition that has differentiated itself from adult-onset MCTD in the last 40 ...two connective tissue disease find- ings at time ...
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Predictors of mortality in connective tissue disease associated pulmonary arterial hypertension: a cohort study
... mixed connective tissue disease ...lung disease (ILD) defined based on extensive disease (> 20% lung involvement) on high-resolution CT lung (HRCT), or evidence of fibrosis on HRCT ...
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Epidemiology of organic solvents and connective tissue disease
... The determination of the solvents to which an individual has been exposed is critical to the reliability of epidemio- logical studies. It is often difficult to infer correctly the exact agent, not only because of the ...
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Original Article Leprosy mimicking connective tissue disease - a challenge for rheumatologists
... for connective tissue disease; 2) leprosy is rare in nonendemic re- gions and has a long incubation period; and 3) the clinicians were not flexible in applying disease classification criteria ...
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A simplified lung ultrasound for the diagnosis of interstitial lung disease in connective tissue disease: a meta analysis
... The PubMed, Embase, and Web of Science databases were searched up to October 31, 2018. Two investigators independently searched the databases and screened the ar- ticles. Disagreements were resolved by a third ...
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Mixed connective tissue disease: state of the art on clinical practice guidelines
... Mixed connective tissue disease (MCTD) is a complex overlap disease with features of different autoimmune connective tissue diseases (CTDs) namely systemic sclerosis, ...
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Fibrosis in connective tissue disease: the role of the myofibroblast and fibroblast epithelial cell interactions
... There has been much speculation on the origin of activated fibroblasts in the skin of SSc patients and what influences their differentiation toward a myofibroblast phenotype. There is evidence that activated fibroblasts ...
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A confocal microscopy study of anticytoskeletal antibody activity in patients with connective tissue disease.
... While confirming the results of previous immunofluorescence studies which have shown that autoantibodies that bind to filamentous structures in the cytoplasm of cultured cells are common[r] ...
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Thrombotic Thrombocytopenic Purpura Associated with Mixed Connective Tissue Disease: A Case Report
... TTP associated with mixed connected tissue disease is rare and has only been described in nine patients (Table 2) [13–21]. Most of these cases were women (8 : 1) with the median age of 40 years. The ...
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Immunology and Disease of Connective Tissue
... single- or double-stranded DNA: the peripheral or ring pattern, usually indicating the presence of anti bodies to double-stranded DNA with active lupus present, usually with renal involvement: the nucleolar pattern, in ...
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Usefulness of surgical lung biopsies after cryobiopsies when pathological results are inconclusive or show a pattern suggestive of a nonspecific interstitial pneumonia
... cHP: chronic hypersensitivity pneumonia; CTD-ILD: connective tissue disease-associated interstitial lung disease; DIP: desquamative interstitial pneumonia; DPLD: diffuse parenchymal lung[r] ...
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Pulmonary hypertension in systemic sclerosis and systemic lupus erythematosus
... positive connective tissue diseases ...other connective tissue diseases, including SSc-SLE over- lap syndrome [3], mixed connective tissue disease (MCTD) [4–6], ...
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Relationship between fibroblastic foci profusion and high resolution CT morphology in fibrotic lung disease
... the connective tissue disease related fibrotic NSIP group, 15 cases were assigned an FFscore of zero by at least one pathologist (10 by both ...nective tissue disease related fibrotic ...
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