Fibrous dysplasia
Imaging in fibrous dysplasia
... Fibrous dysplasia (FD) is a developmental non hereditary osseous disorder. It is often observed in childhood but presents throughout life. The osseous structure is destroyed and is replaced by ...
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Monostotic fibrous dysplasia of temporal bone: a case series and literature review
... Fibrous dysplasia is a benign condition primarily affecting the bone. Pathologically, there is fibrosseous proliferation where normal bone gets replaced with fibrous tissue and immature bone. There ...
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Dedifferentiated chondrosarcoma arising in fibrous dysplasia: A case report and review of the current literature
... Background: Fibrous dysplasia is an uncommon bone disease that has rare but clear potential for malignant transformation. The frequency is increased in polyostotic forms, McCune–Albright syndrome, ...
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Monostotic fibrous dysplasia at C7 treated with vertebroplasty: a case report and review of the literature
... Our literature review revealed only 7 patients (includ- ing the 1 patient reported in this study) who underwent VP for the treatment of spinal fibrous dysplasia, as shown in Table 2 [20, 23, 29–31]; 2 ...
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FGF 23 in fibrous dysplasia of bone and its relationship to renal phosphate wasting
... FGF-23, a novel member of the FGF family, is the product of the gene mutated in autosomal dominant hypophosphatemic rickets (ADHR). FGF-23 has been proposed as a circulating factor causing renal phosphate wasting not ...
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Case Report Management of cerebrospinal fluid leakage in combination with craniofacial fibrous dysplasia
... Abstract: Fibrous dysplasia is a benign bone disorder that most commonly affects craniofacial bones; one or mul- tiple adjacent bones can be involved which can severely deform the skull ...craniofacial ...
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Different clinical presentation and management of temporal bone fibrous dysplasia in children
... Background: Fibrous dysplasia is a slowly progressive benign fibro-osseous disorder that involves one or multiple bones with a unilateral distribution in most ...regarding fibrous dysplasia ...
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First two cases of craniomaxillofacial fibrous dysplasia from Nepal – case series
... Abstract: Fibrous dysplasia is a benign fibro-osseous disease of the bone, which is most com- monly associated with congenital mutations in cAMP regulating protein Gsα coded by GNAS-1 ...craniomaxillofacial ...
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Midfacial degloving approach for management of the maxillary fibrous dysplasia: a case report
... Monostotic fibrous dysplasia, characterized by the in- volvement of only one bone with no systemic manifesta- tions, is the most common form of this ...
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Illness Perceptions are Associated with Quality of Life in Patients with Fibrous Dysplasia.
... In comparison with the reference groups, personal and treatment control were the most prevalent negative illness perceptions in FD patients, indicating that these patients experience very little control over the course ...
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An epidemiological and clinical analysis of craniomaxillofacial fibrous dysplasia in a Chinese population
... Fibrous dysplasia is a benign and rare bone disorder that often affects the craniofacial skeleton [7]. It usually cause significant morphological and functional disturbance, such as malocclusion, ...
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Advanced Unilateral Fibrous Dysplasia of the Scapula: A Rare Clinical Entity and Surgical Challenge
... Tumors affecting the scapula are uncommon. They represent about 3–4% of all bony tumors [1]. Fibrous dysplasia (FD) is a rare, benign tumor of bone. Overall, FD makes up between 5 and 7% of all benign bone ...
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Individualized approach to the surgical management of fibrous dysplasia of the proximal femur
... of fibrous dysplasia has been very challenging ever since the disease was first described, not the least because of the wide and heterogeneous clinical spectrum of fibrous dysplasia, but also ...
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Craniofacial fibrous dysplasia associated with McCune-Albright syndrome: challenges in diagnosis and treatment: case reports
... The work up done on the patient included histopatho- logical analysis, skeletal survey (CT scan of craniofacial region and a skeletal survey of the body by conventional radiographs). Also complete blood count, calcium ...
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Monostotic fibrous dysplasia of a lumbar vertebral body with secondary aneurysmal bone cyst formation: a case report
... monostotic fibrous dysplasia of the fourth lumbar vertebral ...of fibrous dysplasia superimposed by the formation of aneurysmal bone cyst ...monostotic fibrous dysplasia with ...
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Fibrous Dysplasia of the Maxillofacial Region, a Review of 134 cases at Lagos University Teaching Hospital, Lagos, Nigeria
... 4. Albright F, Butler a M, Hampton a O, et al. Syndrome characterized by osteitis fibrosa disseminata, areas of pigmentation and endocrine dysfunction, with precocious puberty in females: report of five cases. N Engl J ...
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A Rare Case of Monostotic Spinal Fibrous Dysplasia Mimicking Solitary Metastatic Lesion of Thyroid Carcinoma
... The patient underwent posterior decompression with fusion and stabilization of T10-L2 vertebrae with pedicle screw system following deterioration in the symptoms. The indications for decompression were mainly for neural ...
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A Case of Fibrous Dysplasia with Bilateral Shepherd Crook Deformity Treated with Dynamic Hip Screw Fixation
... Case Report: A 22-year-old male known case of polyostotic fibrous dysplasia presented with bilateral shepherd’s crook deformity of the proximal femur. Preoperatively, neck-shaft angle was 15° on the right ...
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Surgical treatment for fibrous dysplasia of femoral neck with mild but prolonged symptoms: a case series
... with fibrous dyspla- sia of the femoral neck, prospectively and consecutively treated with identical methods in all nine hips, namely autogenous fibular strut grafting combined with ...for fibrous ...
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Original Article A case of secondary chondrosarcoma with TP53 mutation arising from fibrous dysplasia
... [2] Boyce AM, Collins MT. Fibrous Dysplasia/ McCune-Albright Syndrome. In: Pagon RA, Adam MP, Ardinger HH, Wallace SE, Amemiya A, Bean LJH, Bird TD, Fong CT, Mefford HC, Smith RJH, Stephens K, editors. ...
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