Fructose intolerance
Pitfalls in the Diagnosis of Hereditary Fructose Intolerance
... that fructose intolerance may not be pathognomonic for HFI alone, given the description of rare patients with fruit-induced, food protein–induced enterocolitis ...
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Hereditary Fructose Intolerance in the Vomiting Infant
... consideration of hereditary fructose intolerance in any infant who vomits and has a diet containing fructose. A high index of suspicion and a general knowledge of fructose-containing sub[r] ...
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Isolation and characterization of a mutant liver aldolase in adult hereditary fructose intolerance Identification of the enzyme variant by radioassay in tissue biopsy specimens
... Hereditary fructose intolerance (HFI) is a metabolic disorder caused by enzymic deficiency of aldolase B, a genetically distinct cytosolic isoenzyme expressed exclusively in liver, kidney, and ...whom ...
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An experimental renal acidification defect in patients with hereditary fructose intolerance: I Its resemblance to renal tubular acidosis
... hereditary fructose intolerance (HFI), but in none of five normal subjects, the experimental administration of fructose invariably induced a reversible dysfunction of the renal tubule with ...
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Fruit-Induced FPIES Masquerading as Hereditary Fructose Intolerance
... Hereditary fructose intolerance (HFI) symptoms develop at fi rst in- troduction of fruit during weaning. We report on an infant with sus- pected HFI who presented with repeated episodes of vomiting and ...
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An experimental renal acidification defect in patients with hereditary fructose intolerance: II Its distinction from classic renal tubular acidosis; its resemblance to the renal acidification defect associated with the fanconi syndrome of children with cystinosis
... hereditary fructose intolerance (HFI) fructose induces a renal acidification defect characterized by (a) a 20-30% reduction in tubular reabsorption of bicarbonate (T HCO 3 - ) at plasma bicarbonate ...
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HEREDITARY FRUCTOSE INTOLERANCE IN A PEDIATRIC CONTEXT
... The theoretical reference was elaborated by means of the collection of relevant scientific articles on the subject, made in the electronic databases: Scientific Electronic Library Online (SciELO), Pubmed, EBSCOhost and ...
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Pitfalls in the Diagnosis of Hereditary Fructose Intolerance
... that fructose intolerance may not be pathognomonic for HFI alone, given the description of rare patients with fruit-induced, food protein–induced enterocolitis ...
9
Tagatose: A Low Calorie Multifunctional Sweetener
... hereditary fructose intolerance (HFI) since it is metabolized the same way as fructose, but accidental intake of small amounts of tagatose from commercial products is not likely ...of fructose ...
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The Prognosis of Asthma in Infancy
... regular diet, amounts sufficient to give a posi- tive test for reducing sugar in the routine ex- amination are known to occur only in essential fructosuria, familial fructose intolerance[r] ...
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Genetic determinants of statin intolerance
... Background: Statin-related skeletal muscle disorders range from benign myalgias – such as non- specific muscle aches or joint pains without elevated serum creatinine kinase (CK) concentration – to true myositis with ...
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Health implications of fructose consumption: A review of recent data
... of fructose- sweetened beverages providing 25% of energy requirements for 10 weeks in overweight and obese subjects on visceral adiposity, plasma lipids and insulin ...that fructose or glucose represented ...
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Molecular analysis of the fructose transporter gene (GLUT5) in isolated fructose malabsorption
... a fructose free diet, with relapse upon ...during fructose breath testing is as- sociated with symptoms, whereas breath hydrogen is not ele- vated after ingestion of other test sugars and symptoms do not ...
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Fructose Tolerance in Tay-Sachs' Disease
... istic of time response of patients with hereditary fructose iimtoleraimce. The hepatic fructose-i-. phosphate aldolase activity iIl Tay-Sachs’ dis-[r] ...
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Broad phenotypic spectrum and genotype-phenotype correlations in GMPPB-related dystroglycanopathies: an Italian cross-sectional study
... exercise intolerance and four (P8, P11, P12, P13) easy fatigability; anyway only P8 received pharma- cological treatment showing a partial response to pyrido- ...
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Added fructose as a principal driver of non-alcoholic fatty liver disease: a public health crisis
... rats. Forty-nine male Sprague-Dawley rats weighing 200±20 g were studied. The rats were randomly divided into five groups. One group continued to be maintained on standard rat chow diet (SRCD) for 5 weeks, whereas the ...
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Debt intolerance: Executive summary
... circumstances has it been possible for countries to grow out of their debts; the only available example is provided by Swaziland in 1985. Foreign debt reversals, defined as a decline of 25 or more percentage points of ...
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Pediatric Disorders of Orthostatic Intolerance
... Orthostatic intolerance (OI), having difficulty tolerating an upright posture because of symptoms or signs that abate when returned to supine, is common in ...
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Q&A: 'Toxic' effects of sugar: should we be afraid of fructose?
... metabolites. Fructose metabolism in the liver increases uric acid synthesis, and the ensuing hyperuricemia can secondarily be responsible for endothelial cell dysfunction, impaired insulin-induced vasodilation and ...
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Mechanistic studies on glucose fructose oxidoreductase from Zymomonas mobilis : a thesis presented in partial fulfilment of the requirements for the degree of Master of Science in biochemistry at Massey University, New Zealand
... Glucose-fructose oxidoreductase oxidized or reduced was incubated with substrates: glucose, fructose and sorbitol, and DEPC before the enzyme activity was measured... The oxidised form o[r] ...
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