Histiocytosis X
Histiocytosis X Purified (T6+) cells from bone granuloma produce interleukin 1 and prostaglandin E2 in culture
... cell-like histiocytosis X cells predominantly found in the bone lesions, we have purified T6+ cells by the use of a fluorescence-activated cell ...of histiocytosis X ...that ...
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Healing Rates of Treated and Untreated Bone Lesions in Histiocytosis X
... Healing Rates of Treated and Untreated Bone Lesions in Histiocytosis X. http://pediatrics.aappublications.org/content/76/2/286[r] ...
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Letterer-Siwe's Disease (Acute Disseminated Histiocytosis X): A Case Complicated by Disseminated Intravascular Coagulation and Responding to Heparin Therapy
... Disseminated Intravascular Coagulation and Responding to Heparin Therapy Letterer-Siwe's Disease (Acute Disseminated Histiocytosis X): A Case Complicated by. Services[r] ...
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GENETIC DETERMINATION OF ACUTE DISSEMINATED HISTIOCYTOSIS X (LETTERER-SIWE SYNDROME)
... The disease in both twins was not only consistent with, but also quite characteristic of, the acute disseminated form of histiocytosis X-the Letterer-Siwe syndrome-ex- cept for the exten[r] ...
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Pulmonary Langerhans cell histiocytosis X: an analysis of four cases
... (PLHH) X; langerhans hücreli histiositozisin alt grubu olup akciğer- lerde langerhans hücre infiltrasyonunun görüldüğü, nedeni bilinmeyen, en sık 20–40 yaşları arasında görü- len nadir bir interstisyel akciğer ...
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BRAF in LCH tissue samples. Intraoperative squash smears of a small tissue fragment excised from the lesion
... cell histiocytosis (LCH) is a rare dis- ease that accounts for less than 1% of all tumor-like lesions of bone mainly affecting the skull, femur, mandible and ribs ...as histiocytosis X with 3 ...
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Rare Langerhans cell histiocytosis in children: a case report
... cell histiocytosis (LCH) is a rare disease, formally known as histiocytosis X that is characterized by abnormal proliferation of histiocytes derived from bone marrow (Langerhans cells), joined with ...
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Oral manifestation of Langerhans cell histiocytosis: a case report
... cell histiocytosis (LCH), formerly known under a variety of different names such as histiocytosis X, eosinophilic granuloma, Hand-Schüller-Christian dis- ease or Letterer-Siwe disease, is a rare ...
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Langerhans Cell Histiocytosis Presenting as Uncontrolled Asthma
... cell histiocytosis (LCH) is an uncommon disor- der affecting primarily young adult smokers ...cell histiocytosis can affect the lungs in isolation or as part of a systemic disease affecting the bones, ...
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Long term sequelae of multisystem Langerhans' cell histiocytosis
... by histiocytosis in the 'active' phase is well recognised and relatively ...‘histiocytosis X' appeared in 1935 (Lederer, Poncher, & Fabricant ...
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Imaging of langerhans histiocytosis - Pictorial essay
... Langerhans histiocytosis (LCH) is a group of unknown disorders, characterized by the presence of cells with characteristics similar to bone marrow derived langerhans ...term histiocytosis X, since ...
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Skeletal involvement in Langerhans cell histiocytosis
... “histiocytosis X”, a term that grouped three major syndromes, which are now considered as clinical variants of the same disease: the eosinophilic granu- loma (unifocal LCH with a solitary bone lesion), the ...
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Langerhans cell histiocytosis presenting as isolated central diabetes insipidus in a 2-year-old child: a rare manifestation of rare disease
... 2. Marchand I, Barkaoui MA, Garel C, Polak M, Donadieu J, Writing Committee. Central diabetes insipidus as the inaugural manifestation of Langerhans cell histiocytosis: natural history and medical evaluation of 26 ...
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Case Report Erdheim-Chester Disease with Involvement of Axial Skeleton: A Rare Presentation of Rare Disease
... Girerd X, Weber N, Piette JC, Grenier PA, et al: Pulmonary involvement in Erdheim- Chester disease: a single-center study of thirty-four patients and a review of the ...
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Retrospective analysis of clinical manifestations and treatment outcomes of patients diagnosed with langerhans cell histiocytosis from a tertiary cancer hospital in South India
... In another retrospective analysis done in Children’s Hospital New Orleans during 2005-2014, a total of 41 patients who were diagnosed and treated for Langerhans cell histiocytosis were studied. The distribution by ...
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Isolated Sphenoid Sinus Lesions: Experience with a Few Rare Pathologies.
... showed a well‑defined homogenously enhancing sphenoid sinus lesion. Extending superiorly and on both sides. MRI showed T1‑hypo‑isointemse, T2‑hyper‑isointense, and heterogeneously enhancing mass in sphenoid sinus. ...
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The natural history of adult pulmonary Langerhans cell histiocytosis: a prospective multicentre study
... This prospective, multicentre study was conducted by the French National Reference Centre for Langerhans Cell Histiocytosis, in collaboration with six hospital pulmonary departments. The inclusion period was from ...
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Effectiveness of cladribine therapy in patients with pulmonary Langerhans cell histiocytosis
... The results suggested a greater treatment effect in subjects with nodular lung lesions and/or thick-walled cysts on chest HRCT, with diffuse hypermetabolism of lung lesions on positron e[r] ...
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Pulmonary Langerhans Cell Histiocytosis Imitating Metastatic Lung Carcinoma
... Pulmonary Langerhans cell histiocytosis (PLCH) is a rarely seen disease. We think our case is worthy of publication due to its presentation with anamnesis and clinical findings very similar to metastatic pulmo- ...
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Langerhans cell histiocytosis in adults: a case report and review of the literature
... Case report: A case of rare adult LCH was reported and the clinicopathological features were summarized by literature review. The multifocal form of this case includes diabetes insipidus, exophthalmos and mucocutaneous ...
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