Juvenile dermatomyositis
Staphylococcus aureus Panniculitis Complicating Juvenile Dermatomyositis
... juvenile dermatomyositis. The 3 previously reported cases of juvenile dermatomyositis and panniculitis were attributed to flare of underlying disease, rather than infection, and were treated ...
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Endothelial progenitor cell number is not decreased in 34 children with Juvenile Dermatomyositis: a pilot study
... DM/PM: Dermatomyositis and polymyositis; DUD: Duration of untreated disease; EPC: Endothelial progenitor cells; ERL: End row loop; FACS: Fluorescence activated cell sorting; FMO: Fluorescence minus one; HDL: ...
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Efficacy of thalidomide in a girl with inflammatory calcinosis, a severe complication of juvenile dermatomyositis
... The effect of infliximab in refractory calcinosis with juvenile dermatomyositis was reported previously [7]. The anti-TNF-alpha biologics such as infliximab and etanercept are designed specifically to ...
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Effectiveness of Rituximab Therapy on Severe Calcinosis in 4 Children with Juvenile Dermatomyositis
... Juvenile dermatomyositis (JDM) is a rare disease but it is the most common in- flammatory myopathy in children. It is an autoimmune vasculopathy which primarily affects skin and proximal striated muscles. ...
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<p>Multispecialty approach for improving outcomes in juvenile dermatomyositis</p>
... Juvenile dermatomyositis (JDM) is strongly associated with immune-related genes of human leukocyte antigen region. Characteristic abnormalities include excess type I interferon production in blood and ...
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Development of an internationally agreed minimal dataset for juvenile dermatomyositis (JDM) for clinical and research use
... and juvenile dermatomyositis, polymyositis, and inclusion body myositis: Physician and Patient/Parent Global Activity, Manual Muscle Testing (MMT), Health Assessment Questionnaire (HAQ)/Childhood Health ...
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Safety of Intravenous Immunoglobulin in the Treatment of Juvenile Dermatomyositis: Adverse Reactions Are Associated With Immunoglobulin A Content
... We sought to determine whether different intravenous immu- noglobulin products used in the treatment of juvenile dermatomyositis are equally well tolerated by patients and, if not, wheth[r] ...
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Safety of Intravenous Immunoglobulin in the Treatment of Juvenile Dermatomyositis: Adverse Reactions Are Associated With Immunoglobulin A Content
... We sought to determine whether different intravenous immu- noglobulin products used in the treatment of juvenile dermatomyositis are equally well tolerated by patients and, if not, wheth[r] ...
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Myeloid related protein induces muscle derived inflammatory mediators in juvenile dermatomyositis
... The Juvenile Dermatomyositis Research Group would like to thank all of the patients and their families who contributed to the Juvenile Dermatomyositis Cohort ...
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Ovarian Teratoma Mimicking Features of Juvenile Dermatomyositis in a Child
... An 8-year-old girl complained for 4 months of right arm pain, weakness in both legs, difficulty in arising from a seated or squatting position, and 1 month of pain in her hips, ankles, and knees. On physical exam- ...
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Methods for analyzing observational longitudinal prognosis studies for rheumatic diseases: a review & worked example using a clinic-based cohort of juvenile dermatomyositis patients
... We will use Juvenile Dermatomyositis (JDM) as a con- venient disease model to show how longitudinal de- sign and analysis can be used in rheumatic diseases. Multiple cross-sectional studies have determined ...
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Thrombotic Microangiopathy and Purtscher-like Retinopathy as a Rare Presentation of Juvenile Dermatomyositis
... Juvenile dermatomyositis is a rare systemic vasculopathy that may sometimes present with acute ...severe dermatomyositis associated with throm- bocytopenia and blurry ...severe juvenile ...
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MRI guided wire localization muscle biopsy in a child with juvenile dermatomyositis
... Juvenile dermatomyositis is an autoimmune, inflamma- tory myopathy. Though a rare disease, it is the most common inflammatory myopathy in children with an in- cidence of 2–3 cases per million children per ...
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Muscle MRI at the time of questionable disease flares in Juvenile Dermatomyositis (JDM)
... Juvenile dermatomyositis (JDM) is a chronic multisys- tem disease of presumed autoimmune origin. JDM is the most common of the idiopathic inflammatory my- opathies of childhood, comprising 85% of cases [1]. ...
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Clinical phenotypes and biologic treatment use in juvenile dermatomyositis-associated calcinosis
... As the most common inflammatory myopathy of child- hood, Juvenile Dermatomyositis (JDM) affects 3.2 per million children annually in the United States [1]. Before the widespread use of glucocorticoids, ...
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Developing a provisional, international Minimal Dataset for Juvenile Dermatomyositis: for use in clinical practice to inform research
... The Juvenile Dermatomyositis Cohort Biomarker Study and Repository, UK and Ireland (JDCBS) provides a large pro- spective collection of juvenile idiopathic inflammatory myopathies (currently >430 ...
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Anti MDA5 autoantibodies in juvenile dermatomyositis identify a distinct clinical phenotype: a prospective cohort study
... Patient serum samples and clinical data were obtained through the UK Juvenile Dermatomyositis Cohort and Biomarker Study (JDCBS). The JDCBS is a large cohort of UK patients with myositis, the majority with ...
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Being on the Juvenile Dermatomyositis Rollercoaster: a qualitative study
... Juvenile Dermatomyositis is a rare condition typically managed in specialist centres around the ...as Juvenile Idiopathic Arthritis ...for juvenile arthritis ...
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Subcutaneous Immunoglobulin in Refractory Juvenile Dermatomyositis
... 2. Huber AM, Giannini EH, Bowyer SL, et al. Protocols for the initial treatment of moderately severe juvenile dermatomyositis: results of a Children’s Arthritis and Rheumatology Research Alliance Consensus ...
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Adult and juvenile dermatomyositis: are the distinct clinical features explained by our current understanding of serological subgroups and pathogenic mechanisms?
... The Juvenile Dermatomyositis Research Group would like to thank all of the patients and their families who contributed to the Juvenile Dermatomyositis Cohort ...
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