long chain
Fatal pitfalls in newborn screening for mitochondrial trifunctional protein (MTP)/long-chain 3-Hydroxyacyl-CoA dehydrogenase (LCHAD) deficiency
... At the age of 4 months, after an episode of vomiting and reduced food intake, the patient suffered a life-- threatening metabolic decompensation. He presented with hypoglycemia, lactic acidosis (lactate 5 mmol/l; ...
8
Synthesis of long chain fatty acids and some derivatives
... of long-chain acids is by reaction of the unsaturated acids with oxygen, alone, in the presence of catalyst, o r under the influrence of a ...to long-chain ...
149
Extension of Linear Isotherm Regularity to Long Chain Alkanes
... to long chain organic compounds using the group contribution method ...as long chain organic compounds, show some deviation from the linear behaviour of the ...
8
Very long-chain fatty acids support synaptic structure and function in the mammalian retina
... very long chain fatty acids clearly provoked changes in the membrane structure of presynaptic photoreceptor terminals, causing them to with- draw into the ONL away from the bipolar cell dendrites, creat- ...
7
Gastric Lipolysis and Fat Absorption in Preterm Infants: Effect of Medium-Chain Triglyceride or Long-Chain Triglyceride-Containing Formulas
... The study showed that (1) there was marked hydrolysis of formula fat in the stomach during feeding of either medium-chain triglyceride formula or long-chain triglyceride formula (20% and[r] ...
9
Long-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency: Clinical Presentation and Follow-Up of 50 Patients
... hypotonia, and feeding difficulties. Careful analysis of the clinical history of those patients presenting with acute hypoglycemia revealed that 32 (82%) of the 39 patients already had a combination of nonspe- cific ...
8
QUANTIFICATION OF LONG CHAIN MONO AND POLYUNSATURATED FATTY ACIDS
... In this work are presented various chromatographic systems, TLC, HPLC, GC, designed to identify and accurately quantify the long-chain mono- and polyunsaturated fatty acids of different samples with a focus ...
5
A comparison of pain on intravenous injection to two formulations of Propofol, one containing medium chain and long chain triglycerides and the other without medium chain and long chain triglycerides
... In one such formulation of Propofol [with MCT/LCT], the oil phase consists of medium chain triglycerides (MCT) and long chain triglycerides (LCT). Such a composition, results in smaller ...
8
The role of vitamin D and Omega 3 long chain polyunsaturated fatty acids in children with Autism Spectrum Disorder : a thesis presented in partial fulfilment of the requirements for the degree of Doctor of Philosophy in Nutritional Science, Massey University, Albany, New Zealand
... Paper V Mazahery, H., C. Conlon, K.L. Beck, O. Mugridge, M.C. Kruger, W. Stonehouse, C.A. Camargo, Jr., B.J. Meyer, B. Tsang, B. Jones, and P.R. von Hurst, A randomised controlled trial of vitamin D and omega-3 ...
16
A Late Quaternary climate record based on long-chain diol proxies from the Chilean margin
... applied long-chain diols as tracers for past SST (us- ing the LDI), upwelling and nutrient conditions (diol index), and [PO 3− 4 ] and [NO − 3 ] (NDI) at ODP 1234, located within the Peru–Chile upwelling ...
21
Intestinal Long Chain Fatty Acids Act as a Direct Signal To Modulate Expression of the Salmonella Pathogenicity Island 1 Type III Secretion System
... ABSTRACT Salmonella enterica serovar Typhimurium uses the Salmonella pathogenicity island 1 (SPI1) type III secretion sys- tem (T3SS) to induce inflammatory diarrhea and bacterial uptake into intestinal epithelial cells. ...
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Treatment of cardiomyopathy and rhabdomyolysis in long chain fat oxidation disorders using an anaplerotic odd chain triglyceride
... of long-chain fat oxidation ...other long-chain fat oxidation disorders, including VLCAD deficiency, is designed to (a) reduce the amount of long-chain dietary fat while covering ...
12
Phase Transitions of Long-Chain N-Alkanes at Interfaces
... if the degree of confinement is reduced by separation of the mica surfaces. An increase in the area of the liquid-vapour interface relative to that of the liquid-mica interface facilitates freezing in the case of the ...
8
Long chain fatty acids of peptococci and peptostreptococci
... This study presents an analysis of the long- streptococcus micros, Peptostreptococcus productus, chain fatty acids LCFAs extracted from the Peptostreptococcus parvulus, Peptococcus asacc[r] ...
7
Occurence and reactions of long chain epoxy acids
... A stock solution of monoperphthalic acid in ether 500ml containing 0.22mole peracid, prepared by the standard prodedure^^?, was stored at 0^0 over anhydrous sodium sulphate, Olive oil me[r] ...
208
Medium and long chain fat absorption in patients with cirrhosis
... In addition, although nearly one-third of the cirrhotic patients groups B2 and B3 showed varying degrees of malabsorption of LCT, the mean absorption rate of a medium chain fatty acid oc[r] ...
10
Crystallisation and chain conformation of long chain n alkanes
... We tried to observe conformational changes related to the tilting of the n-alkane chains inside the crystals of sample (1) using infrared spectroscopy. Infrared spectra were recorded at elevated temperatures and at ...
264
Cryptosporidium parvum Long-Chain Fatty Acid Elongase
... alkyl chain of cerulenin could be too long to bind to the active site of the enzyme (15), or (ii) the active site serving as the target of cerulenin could be somewhat inacces- sible due to the extreme ...
11
The role of epidermal sphingolipids in dermatologic diseases
... Several hypotheses might explain the cause of cer- amide deficiency observed in the stratum corneum of AD patients. It is suggested that the activity of sphingo- myelin glucosylceramide deacylase, an enzyme which ...
9
Early postoperative changes of sphingomyelins and ceramides after laparoscopic sleeve gastrectomy
... with long chain plasma ceramides ...in long chain ceramide species corre- lated significantly with TNF-α levels at 6 months follow- ing gastric bypass surgery ...
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