Paraneoplastic pemphigus
Paraneoplastic pemphigus and myasthenia gravis as the first manifestations of a rare case of pancreatic follicular dendritic cell sarcoma: CT findings and review of literature
... After a multidisciplinary discussion, the patient ’ s tenta- tive diagnosis was paraneoplastic pemphigus and the myasthenia symptoms caused by the pancreatic tumor. Myasthenia gravis, in turn, led to the ...
7
Paraneoplastic Autoimmune Multiorgan Syndrome (Paraneoplastic Pemphigus) in a Child: Case Report and Review of the Literature
... ABSTRACT. Paraneoplastic autoimmune multiorgan syndrome, also known as paraneoplastic pemphigus, has been observed only rarely among ...of paraneoplastic pemphigus associated with ...
6
Antibodies against desmoglein 3 (pemphigus vulgaris antigen) are present in sera from patients with paraneoplastic pemphigus and cause acantholysis in vivo in neonatal mice
... Paraneoplastic pemphigus (PNP) is an autoimmune blistering disease that occurs in association with underlying ...of pemphigus vulgaris and pemphigus ...
9
Case Report Adrenal Castleman disease associated with paraneoplastic pemphigus: a case report and literature review
... Abstract: Castleman tumor, a rare lymphoproliferative disorder, is one of the associated tumors in paraneoplastic pemphigus (PNP). Castleman tumor was a frequently reported neoplasm in association with ...
5
Original Article Paraneoplastic pemphigus associated with follicular dendritic cell sarcoma: report of a case and review of literature
... or pemphigus”. Since the prevalence of the Figure 1. Paraneoplastic pemphigus patients with head and neck, chest and abdomen, back of the hand and dorsal pedis skin ...
12
Human autoantibodies against desmoplakins in paraneoplastic pemphigus
... paraneoplastic pemphigus has been described. Paraneoplastic pemphigus is associated with lymphoid malignancies, thymomas, and poorly differentiated ...
9
Paraneoplastic pemphigus: a short review
... Paraneoplastic pemphigus (PNP) is a rare and often fatal autoimmune blistering disease accompanied by both benign and malignant neoplasms. The most frequently reported associated malignancies are ...
5
Rituximab Treatment for Paraneoplastic Pemphigus Associated with Follicular B-Cell Lymphoma: A Case Report and Review of Treatment Outcome
... remission rates were approximately 65-78%. Mean time to disease control was less than one month. The underlying neoplasm of PNP, rather than an autoimmune process, may be a reason for the difference in clinical outcomes ...
6
A Clinico-Epidemiological study of Oral Lesions in Acquired Bullous Dermatoses
... paraneoplastic pemphigus. The mean age of onset is 60 years. 5 Paraneoplastic pemphigus has a poor prognosis with a mortality rate of around ...
158
Download Download PDF
... 1:2. Pemphigus Vulgaris (PV), Pemphigus Vegetans, Pemphigus Foliaceus, Pemphigus Erythematous, Paraneoplastic Pemphigus (PNP) and drug related pemphigus are major variants ...
5
Multicentric Castleman’s disease with voltage-gated potassium channel antibody-positive limbic encephalitis: a case report
... CD most commonly presents with lymphadenopathy in the neck, chest, and/or abdomen. Central nervous system (CNS) involvement is rare, but intracranial, extra-axial lesions mimicking meningiomas have been reported in CD ...
5
Study of HLA DR and DQ Types in Patients with Pemphigus Vulgaris as Compared to that in Healthy Subjects
... 3 patients. Other conditions that were a chance occurrence, seen in one patient each were hepatitis C, HIV, bronchial asthma, atopy and adjustment disorder. Single patient at the time of inclusion had retroperitoneal ...
202
Evaluation the role of direct immunofluorescence techniques and their relevance to the diagnosis of the blistering diseases
... of pemphigus: pemphigus vulgaris (PV), pemphigus vegetans (PVE), pemphigus foliaceus (PF), drug- induced pemphigus (DIP), paraneoplastic pemphigus (PNP), and ...
15
PEMPHIGUS VULGARIS: AN UPDATE ON ETIOPATHOGENESIS, CLINICAL MANIFESTATIONS, DIAGNOSIS AND TREATMENT MODALITIES
... 5.Anhalt G, Kim S, Stanley J et al. Paraneoplastic pemphigus: an autoimmune mucocutaneous disease associated with neoplasia. The New England Journal of Medicine 1990;323(25):1729-1735. 6.Morioka S, Naito K, ...
6
Prediction of survival for patients with pemphigus vulgaris and pemphigus foliaceus: a retrospective cohort study
... Previous studies provided fragmented information suggesting that an older age of onset [3,10,11,13], concomitant involvement of the skin and mucosal surface at early disease presentation [9,14,15], delayed initiation of ...
14
Paraneoplastic Dermatomyositis: A 12 year Retrospective Review in the Department of Dermatology Hospital Kuala Lumpur
... Table I is the summary of all 18 patients with paraneoplastic dermatomyositis. While waiting for the work up for malignancies patients were given prednisolone in the range of 30-75mg/day to treat muscle weakness. ...
5
Distinction between epidermal antigens binding pemphigus vulgaris and pemphigus foliaceus autoantibodies
... To confirm that PF antibodies, which specifically bound to a 160,000-mol wt protein band on immunoblots, were actually pemphigus antibodies, we eluted the IgG from the protein that was c[r] ...
9
Unusual Paraneoplastic Presentation of Cholangiocarcinoma
... Cutaneous paraneoplastic syndromes are a heterogeneous group of skin manifestations that occur in relation to many known ...malignancies. Paraneoplastic occurrence of SCLE has been noted but is not commonly ...
5
Direct Immunofluorescence in Immunobullous disorders of skin with histopathological correlation.
... to pemphigus vegetans, a pseudocarcinomatous hyperplasia of the epidermis, subepidermal bullae, and accumulations of eosinophils and lymphocytes may be seen 10 ...
74
Neonatal Pemphigus Vulgaris
... further maternal transfer of pemphigus antibodies, he or she is not subject to a lasting disease and the clinical signs disappear with no known recurrence;. at Viet Nam:AAP Sponsored on [r] ...
6