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Wegener’s Granulomatosis

A Case of Granulomatosis with Polyangiitis (Wegener’s Granulomatosis) Presenting with Marked Inflamed Tracheobronchial Mucosa

A Case of Granulomatosis with Polyangiitis (Wegener’s Granulomatosis) Presenting with Marked Inflamed Tracheobronchial Mucosa

... A 70-year-old man was admitted to our hospital because of weight loss and persistent dry cough. Chest radiograph and CT showed multiple infiltrates in the bilateral upper lobes and the remarkably thickened bronchial ...

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Rhinologic changes in Wegener's granulomatosis

Rhinologic changes in Wegener's granulomatosis

... Wegener’s granulomatosis is made clinically but the condition may present characteristic features on imaging by CT and ...Wegener’s granulomatosis where the clinical diagnosis may be uncertain and the cANCA ...

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Wegener’s granulomatosis and multiple cranial neuropathies

Wegener’s granulomatosis and multiple cranial neuropathies

... Wegener’s granulomatosis, a term used by a Swedish pathologist, Sven Johnson, who distinguished it from periarteritis nodosa [5] ...Wegener’s granulomatosis featured heavily in an article advocating that ...

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A rare association of chronic lymphocytic leukemia with c ANCA positive Wegener’s granulomatosis: a case report

A rare association of chronic lymphocytic leukemia with c ANCA positive Wegener’s granulomatosis: a case report

... Wegener’s granulomatosis, confirmed by biopsy and by positive c-ANCAs, a situation which is rarely described in the literature [4, 5] in associ- ation with chronic lymphocytic ...

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Gingival hyperplasia as first sign of recurrence of granulomatosis with polyangiitis (Wegener’s granulomatosis): case report and review of the literature

Gingival hyperplasia as first sign of recurrence of granulomatosis with polyangiitis (Wegener’s granulomatosis): case report and review of the literature

... Wegener’s granulomatosis, gingivitis, recur- rent, recurrence” indicated only one report describing the recurrence of GPA without any oral symptoms in the initial presentation of the disease reported by Staines et ...

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A Fatal Case of Treatment Related Adverse Effects in Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)

A Fatal Case of Treatment Related Adverse Effects in Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)

... Well-studied therapies have proven to be effective in treating Granulomatosis with polyangiitis (formerly Wegener’s granulomatosis) (GPA). There has been considerable improvement in survival of patients ...

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Wegener's Granulomatosis - Case Report

Wegener's Granulomatosis - Case Report

... prognosis in Wegener's granulomatosis is generally accepted as worse, although limited and less severe forms of the disease may have better prognosis. Corticosteroid therapy is less effective. A number of cases ...

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Culture-negative subacute bacterial endocarditis masquerades as granulomatosis with polyangiitis (Wegener’s granulomatosis) involving both the kidney and lung

Culture-negative subacute bacterial endocarditis masquerades as granulomatosis with polyangiitis (Wegener’s granulomatosis) involving both the kidney and lung

... of granulomatosis with polyangiitis (GPA) accord- ing to the Chapel Hill Consensus Criteria (1992), although granulomas were not found, possibly due to sampling ...

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Clinical features of childhood granulomatosis with polyangiitis (wegener’s granulomatosis)

Clinical features of childhood granulomatosis with polyangiitis (wegener’s granulomatosis)

... Ozen S, Pistorio A, Iusan SM, Bakkaloglu A, Herlin T, Brik R, Buoncompagni A, Lazar C, Bilge I, Uziel Y, Rigante D, Cantarini L, Hilario MO, Silva CA, Alegria M, Norambuena X, Belot A, Berkun Y, Estrella AI, ...

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Wegener's granulomatosis: current and upcoming therapies

Wegener's granulomatosis: current and upcoming therapies

... T/S has also been studied for its ability to decrease relapses. Stegeman and colleagues conducted a random- ized, placebo, controlled trial in which 81 patients who achieved remission with CYC and prednisone ...

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Wegener's Granulomatosis in the Pediatric Age Group

Wegener's Granulomatosis in the Pediatric Age Group

... Only one pediatric patient described in the liter ature with a classic form of the disease was alive and in remission 39 months after termination of treatment when reported in 1975.h1 Ev[r] ...

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Severe localised granulomatosis with polyangiitis (Wegener’s granulomatosis) manifesting with extensive cranial nerve palsies and cranial diabetes insipidus: a case report and literature review

Severe localised granulomatosis with polyangiitis (Wegener’s granulomatosis) manifesting with extensive cranial nerve palsies and cranial diabetes insipidus: a case report and literature review

... Here we describe a patient with localised but severe granulomatosis with polyangiitis (Wegener ’ s granulomato- sis) manifesting with progressive cranial nerve palsies and pituitary dysf[r] ...

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Time to focus on outcome assessment tools for childhood vasculitis

Time to focus on outcome assessment tools for childhood vasculitis

... vasculitis predominantly according to vessel size, as fol- lows: small [HSP, childhood Wegener’s granulomatosis (c-WG)], medium [KD and childhood polyarteritis nodosa (c-PAN)], and large [childhood Takayasu ...

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Successful endonasal dacryocystorhinostomy in a patient with Wegener’s granulomatosis

Successful endonasal dacryocystorhinostomy in a patient with Wegener’s granulomatosis

... Abstract: Wegener’s granulomatosis (WG) is one form of idiopathic autoimmune vasculitis. The disease has a predilection for the upper and lower respiratory tracts (lungs, nose, sinus), and kidneys. WG may be ...

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Necrotizing Sarcoid Granulomatosis with Pneumothorax

Necrotizing Sarcoid Granulomatosis with Pneumothorax

... sarcoid granulomatosis (NSG) is a rare granulomatous pneumonitis which is composed of a background of sarcoidosis-like granulomas, granulomatous vasculitis, and variable amount of ...Wegener’s ...

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ANCA-Associated Vasculitis: Advancement in
Pathogenesis, Clinical Features and Management

ANCA-Associated Vasculitis: Advancement in Pathogenesis, Clinical Features and Management

... GPA is a rheumatic systemic small vessels inflammation that affects multiple organs and usually accompany with c-ANCA or rarely p-ANCA autoantibodies. The most predominantly affected population category is age bracket of ...

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Granulomatosis with Angitis of Lung treated with Steroids and Rituximab– Case Report and Review of Literature

Granulomatosis with Angitis of Lung treated with Steroids and Rituximab– Case Report and Review of Literature

... Wegener's Granulomatosis and Microscopic Polyangiitis)was a randomized, placebo-controlled, multicenter noninferiority trial that compared induction therapy with rituximab (375 mg/m 2 per week for four weeks) or ...

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Radiotherapy in advanced glottic laryngeal carcinoma in a patient with Wegener’s granulomatosis: how much radiation dose is needed?

<p>Radiotherapy in advanced glottic laryngeal carcinoma in a patient with Wegener&rsquo;s granulomatosis: how much radiation dose is needed?</p>

... 16. Langford CA, Sneller MC, Hallahan CW, et al. Clinical features and therapeutic management of subglottic stenosis in patients with Wegener’s granulomatosis. Arthritis Rheum. 1996;39(10):1754–1760. 17. Neviani ...

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Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia

Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia

... Granulomatosis with polyangiitis (GPA), previously known as Wegener’s granulomatosis, is a pulmonary-renal syndrome affecting small and medium sized blood vessels. The disease has a prevalence in studies ...

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Current and future prospects in the management of granulomatosis with polyangiitis (Wegener&#39;s granulomatosis)

Current and future prospects in the management of granulomatosis with polyangiitis (Wegener&#39;s granulomatosis)

... GPA, granulomatosis with polyangiitis; MPA, microscopic polyangiitis; Plex, plasma exchange; CYCLOPS, Randomized trial of daily oral versus pulse cyclophosphamide as therapy for ANCA-associated systemic ...

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