Wilson’s disease (WD)
Comparative assessment of clinical rating scales in Wilson’s disease
... Currently, there are two clinical rating scales for WD: the Unified Wilson’s Disease Rating Scale (UWDRS) and the Global Assessment Scale for Wilson’s Disease (GAS for WD). The UWDRS has neurological, ...
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Drug induced hepatitis mimicking Wilson’s disease secondary to the use of complex naturopathic regimens: a case report
... All relevant laboratory findings are summarized in Table 2. Initial laboratory investigations revealed signifi- cant transaminitis and decreased synthetic liver function. Her complete blood count was within normal ...
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Spectrum of Hepatic Presentation of Wilsons Disease in Children Attending A Tertiary Care Centre of Dhaka City
... Wilson’s disease, history of immunization against HBV were taken by the ...liver disease (spider angioma, palmer erythema, wasting of thenar and hypothenar muscles), features of acute liver injury (tender ...
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Characteristics of neurological Wilson’s disease with corpus callosum abnormalities
... Forty-one Wilson’ s disease patients who exhibited prom- inent neurological dysfunction were retrospectively ana- lyzed in this study from July 2014 to June 2016 at Wilson’s Disease Centre ...
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Clinical features and outcome in patients with osseomuscular type of Wilson’s disease
... ’ s disease (WD), also known as hepatolenticular de- generation, is an autosomal recessive disease (incidence 1/ 30,000) characterized by Kayser-Fleischer rings of cornea (K-F rings) and multisystem ...
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Neurologic Wilsons Disease and its Management - An Update
... zinc is slow and a period of 4–8 months of treatment is required to reduce copper to nontoxic levels . The dose of the zinc given below (table-II) and each of the dose separated from food & beverages other than water ...
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Fulminant Wilson’s Disease Managed with Plasmapheresis as a Bridge to Liver Transplant
... Laboratory initially revealed mildly elevated transami- nases with increased bilirubin, hypoalbuminemia, and ele- vated international normalized ratio (INR) indicative of hep- atocellular liver injury with impaired liver ...
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Characteristics of a newly diagnosed Polish cohort of patients with neurological manifestations of Wilson disease evaluated with the Unified Wilson’s Disease Rating Scale
... The current study demonstrated a significant correl- ation between disease-related disability (UWDRS Part II) and objective neurological examination (UWDRS Part III). This is consistent with the findings by Oder ...
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Update on the clinical management of Wilson's disease
... Wilson’s disease (WD), albeit relatively rare, is an important genetic metabolic disease because of highly effective therapies that can be ...>500 disease-causing mutations identified, and new ...
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<p>Variants of <em>MIR137HG</em> Genes are Associated with Liver Cancer Risk in Chinese Li Population</p>
... NAFLD, Wilson ’ s disease and other liver ...and Wilson ’ s disease), and the relationship with liver-related diseases are also ...
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The current Status and New Advances in Diagnosis and Treatment of Wilson Disease
... Liver disease may present as tiredness, increased bleeding tendency or confusion (due to hepatic encephalopathy) and portal ...liver disease such as spider naevi (small distended blood vessels, usually on ...
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Clinical Profile of Neurological Manifestations in Wilson Disease
... • One proposed mechanism implicates copper as the inducer of fibrogenesis. Interestingly, hepatocellular carcinoma is exceedingly rare in patients with Wilson’s disease compared to patients with hemochromatosis. ...
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Precision calculation of 1/4-BPS Wilson loops in AdS(5) x S-5
... to Wilson loops with the same topology should cancel measure-related ambiguities is founded on the assumption that the partition function measure is actually not depending on the particular classical solution ...
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The Fusing of Inner Life Theory and Outer Life Theory in Lorraine Hansberry?s A Raisin in the Sun and August Wilson?s Fence
... character. Wilson tries to present the positive image of a responsible black ...merits, Wilson creates a complex character that "subverts the stereotypical view of African American ...Hansberry, ...
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Liver mitochondrial membrane crosslinking and destruction in a rat model of Wilson disease
... the disease, the increase in mitochondrial copper content is paralleled by major structural alterations but only minor functional ...the disease, the mitochondrial copper load exceeds normal levels more ...
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Concordant Pre and Postsynaptic Deficits of Dopaminergic Neurotransmission in Neurologic Wilson Disease
... relations between the SPECT data and the clinical parameters (disease duration, treatment duration, scoring of neurologic symptoms) were tested for linearity. For that, the standard- ized predicted values were ...
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Larviciding to prevent malaria transmission
... cause disease in humans; however, the most impor- tant species in terms of disease burden are Plasmodium falciparum, which is prevalent in sub-Saharan Africa, and Plasmodium vivax, which is more common in ...
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Mowat-Wilson syndrome
... Hirschsprung disease (HSCR), genitourinary anomalies (in particular hypospadias in males), congenital heart defects, agenesis of the corpus callosum and eye ...
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Clinical characteristics and outcomes of hepatocellular carcinoma: results from prospective study, from a tertiary referral center in Sri Lanka
... Upon referral, patient’s clinical history and exa- mination, baseline biochemistry and available imaging were assessed. Hepatocellular carcinoma was diagnosed based on American Association for the Study of Liver ...
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Ethel Wilson and sophistication
... while Wilson rejects the “glossy magazine” kind of sophistica- tion, her biographers have emphasized her soignée ...Ethel Wilson Symposium, commented that in person, Wilson “had an elegance that ...
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