Desmoplastic Small Round Cell Tumor
Case Report Solid-pattern desmoplastic small round cell tumor of the orbit: a case report
... Abstract: Desmoplastic small round cell tumor (DSRCT) is a rare malignancy most commonly originating in the ...sion. Tumor histologically had an entirely solid pattern, lacking ...
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Case Report Beware of immunohistochemistry - report of a cytokeratin-, desmin- and INI-1-negative pelvic desmoplastic small round cell tumor in a 51 year old woman
... Desmoplastic small round cell tumor (DSRCT) was first described by Gerald and Rosai in 1989 [1] and subsequently characterized in a series comprising 19 cases (16 males, 3 females and ...
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Desmoplastic small round cell tumor of the parotid gland-report of a rare case and a review of the literature
... Desmoplastic small round cell tumor (DSRCT) is rare and a highly aggressive neoplasm that typically involves the soft tissues of the abdomen or pelvis in children or young adults, ...
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Antiangiogenic effects in patients with progressive desmoplastic small round cell tumor: data from the French national registry dedicated to the use of off-labeled targeted therapy in sarcoma (OUTC’s)
... Background: Desmoplastic small round cell tumor (DSRCT) is a very rare mesenchymal tumor that mainly affects teenagers and young adults with a mean age at diagnosis around 20–25 ...
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Desmoplastic small round cell tumor of the abdomen: A case report and literature review of therapeutic options
... Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive variety of sarcoma arising typically from abdominal or pelvic peri- ...this tumor and un- derline ...
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Original Article Clinical characteristics and outcomes of abdominal desmoplastic small round cell tumor: a single-center experience of 10 cases
... Background: Desmoplastic small round cell tumor (DSRCT) is a rare and aggressive abdominal tumor typi- cally arising in adolescent and young ...
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A genomic case study of desmoplastic small round cell tumor: comprehensive analysis reveals insights into potential therapeutic targets and development of a monitoring tool for a rare and aggressive disease
... outcomes. Desmoplastic small round cell tumor (DSRCT) is a rare type of sarcoma arising from mesenchymal cells of abdominal peritoneum that usually develops in male adolescents and ...
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Adenosine Transporter ENT4 Is a Direct Target of EWS/WT1 Translocation Product and Is Highly Expressed in Desmoplastic Small Round Cell Tumor
... ENT4 is a member of the equilibrative nucleoside transporter (ENT) family (SLC29), which contains four isoforms [29]. ENT1 and ENT2 transport purine and pyrimidine nucleosides (e.g. uridine, adenosine, etc.) and their ...
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The genomics of desmoplastic small round cell tumor reveals the deregulation of genes related to DNA damage response, epithelial–mesenchymal transition, and immune response
... each tumor-normal pair was correctly matched with a sample concord- ance above 99%; b) levels of cross sample contamination among tumor- normal pairs are ...for tumor samples ranged from 109× to ...
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Desmoplastic small round cell tumors of the pleura: a review of the clinical literature
... Desmoplastic small round cell tumor of the pleura is a rare malignancy, with only a few cases reported in the scientific ...of desmoplastic small round cell ...
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Small blue round cell tumor of the interosseous membrane bearing a t(2;22)(q34;q12)/EWS-CREB1 translocation: a case report
... Merkel cell carcinoma and in rare Ewing family tumors ...clear cell sarcoma, myxoid liposarcoma, extra- skeletal myxoid chondrosarcoma and some Ewing family tumors; desmin is strongly positive in ...
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Primary pulmonary primitive neuroectodermal tumor metastasis to the pancreas: a rare case with seven-year follow-up
... lymphoma, small-cell carcinoma, rhabdomyosar- coma, monophasic synovial sarcoma, and desmoplastic small round cell tumor, all of which are indistinguishable by ...
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Pazopanib in advanced desmoplastic small round cell tumours: a multi-institutional experience
... prominent tumor- associated desmoplasia detected in this disease ...that small molecule tyrosine kinase inhibitors (TKIs) blocking these receptors and their downstream pathways might represent a possible ...
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Use of anlotinib in intra-abdominal desmoplastic small round cell tumors: a case report and literature review
... laparoscopic tumor resection + anterior abdominal wall nodule resection at the Jiangsu Cancer ...the tumor cells were positive for AE1/AE3, desmin, NSE, Ck7, CD34, CD99 and partially positive for CD56, ...
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Desmoplastic small round cell tumour in a 74 year old man: an uncommon cause of ascites (case report)
... In summary, DSRCT is a rare and highly aggressive, cytogenetically unique malignancy. It represents an exceedingly uncommon cause of ascites. The above case shared many features with those previously reported in the ...
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<p>Desmoplastic Reaction and Tumor Budding in Cervical Squamous Cell Carcinoma are Prognostic Factors for Distant Metastasis: A Retrospective Study</p>
... the tumor cell has the potential to disseminate or ...of tumor budding. 11,22 The tumor dedifferentiation phenotypes at the invasive border are a morphologic feature of epithelial- mesenchymal ...
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Case Report Primary cutaneous small cell carcinoma; a case report with differential diagnosis
... SCLC and SmCC of the exptrapulmonary organs very frequently express KIT and PDGFRA. For these, please refer to the author’s numerous publications. In the present study also, the author investigated the gene status of KIT ...
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Case Report Primary pleomorphic liposarcoma of liver: a case report and review of the literature
... nant tumor which originated from mesenchy- mal tissue. This kind of tumor can be occurred in multiple parts of the body, such as extremity, brain, mediastinum, mesentery, in which the extremity accounts for ...
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Letter to Editor Small cell malignant melanoma of the anus: a case report with review of the literature
... signet-ring cell, rhabdoid, and balloon cell [1-6]. Small cell MM is one of the rarest cytomorphological variants, characterized histopathologically by the prolif- eration of small ...
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Case Report Granular cell tumor of the ampulla of Vater: report of a unique case with emphasis on immunohistochemistry for TFE3 antigen expression
... TFE3 tumor family, Roczniak-Ferguson research team [15] have proposed an error in native TFE3 degrada- tion or promoter enhancement resulting in pro- tein ...
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