Granulomatosis with polyangiitis
A rare case report of polyangiitis overlap syndrome: granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis
... with polyangiitis is characterized by necrotizing granulomatous inflammation that usually involves the upper and lower respiratory tracts as well as by necrotizing, crescentic ...
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Severe localised granulomatosis with polyangiitis (Wegener’s granulomatosis) manifesting with extensive cranial nerve palsies and cranial diabetes insipidus: a case report and literature review
... Here we describe a patient with localised but severe granulomatosis with polyangiitis (Wegener ’ s granulomato- sis) manifesting with progressive cranial nerve palsies and pituitary dysf[r] ...
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The role of conjunctival biopsy in the diagnosis of granulomatosis with polyangiitis
... With regard to cases that were diagnosed based on bi- opsy of the conjunctiva in particular, there are only a few case reports in the literature. Karakousis et al. [17] described an 18-year-old boy with scleritis, ...
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Granulomatosis with polyangiitis: a 17 year experience from a tertiary care hospital in Pakistan
... Objective: Granulomatosis with Polyangiitis (GPA) is an autoimmune, multi-system, small and medium vessel vascu- litis with granulomatous ...Keywords: Granulomatosis with polyangiitis, ...
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Sigmoid colon perforation in the patient with granulomatosis with polyangiitis
... with polyangiitis (GPA, formerly known as Wegener’ s granulomatosis) is a systemic anti-neutrophil cytoplasmic antibodies-associated vasculitis that may result in life-threatening organopathies such as ...
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Lung involvement in childhood onset granulomatosis with polyangiitis
... with polyangiitis is an ANCA-associated systemic vasculitis with a low incidence in the pediatric ...by granulomatosis with polyangiitis, both at disease ’ s onset and during ...
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Granulomatosis with polyangiitis presenting as an orbital inflammatory pseudotumor: a case report
... Granulomatosis with polyangiitis (GPA), formerly called Wegener ’ s granulomatosis, was first described by Heinz Klinger in 1932. GPA usually presents as a triad of airway necrotizing granulomas, ...
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Eosinophilic Granulomatosis with Polyangiitis: Experiences in Korean Patients
... Eosinophilic granulomatosis with polyangiitis (EGPA) is one form of antineutrophil cytoplasmic antibody (ANCA)-associated vascu- litis. Identical to what has been called Churg-Strauss syndrome, EGPA ...
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Childhood-onset granulomatosis with polyangiitis and microscopic polyangiitis: systematic review and meta-analysis
... Eosinophilic granulomatosis with polyangiitis (Churg-Strauss); EMA: European medicines agency; ENT: Ear, nose and throat; ESRD: End-stage renal disease; EULAR: European league against rheumatism; FDA: Food ...
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<p>Transient Eosinophilic Granulomatosis with Polyangiitis-Like Vasculitis During Omalizumab Therapy: A Case Report</p>
... eosinophilic granulomatosis with polyangiitis (EGPA), however different reports described the occurrence of EGPA while on omalizumab in patients with asthma or vasculitic ...
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IgG4:IgG RNA ratio differentiates active disease from remission in granulomatosis with polyangiitis: a new disease activity marker? A cross sectional and longitudinal study
... Table 1 Patient characteristics and disease activity parameters in total granulomatosis with polyangiitis cohort, active patients as determined by Birmingham Vasculitis Activity Score ≥ [r] ...
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Necrobiotic xanthogranuloma scleritis in a case of granulomatosis with polyangiitis (Wegener’s granulomatosis)
... with granulomatosis with polyangiitis based on granuloma found in scleral tissue, vasculitis seen in sural nerve biopsy and positive serologies (C-ANCA and anti-PR3 ...of granulomatosis with ...
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A Case of Granulomatosis with Polyangiitis (Wegener’s Granulomatosis) Presenting with Marked Inflamed Tracheobronchial Mucosa
... A 70-year-old man was admitted to our hospital because of weight loss and persistent dry cough. Chest radiograph and CT showed multiple infiltrates in the bilateral upper lobes and the remarkably thickened bronchial ...
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Successful rituximab treatment of granulomatosis with polyangiitis with cranial neuropathies
... In granulomatosis with polyangiitis (GPA), peripheral nerve involvement is common but central nervous system (CNS) involvement is extremely rare and treatment strategy has not been ...
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An uncommon presentation of eosinophilic granulomatosis with polyangiitis: a case report
... Churg–Strauss syndrome or, as recently renamed, eosi- nophilic granulomatosis with polyangiitis (EGPA) [1], is a rare and potentially fatal disease, with an annual inci- dence ranging between 0.5 and 6.8 ...
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Aberrant cytokine pattern of the nasal mucosa in granulomatosis with polyangiitis
... GPA: Granulomatosis with polyangiitis; IFN- γ : interferon- γ ; IL: interleukin; JNK: JUN- N terminal protein kinase; MAPK: mitogen-activated protein kinase; MCP-1: monocyte chemotactic protein-1; MIP-1: ...
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Exclusively ocular and cardiac manifestation of granulomatosis with polyangiitis – a case report
... Background: Granulomatosis with polyangiitis (GPA) is an antineutrophil cytoplasmic antibodies (ANCA)-associated necrotizing granulomatous vasculitis that affects small to medium size ...
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Familial Eosinophilic Granulomatosis with Polyangiitis
... Eosinophilic Granulomatosis with Polyangiitis (EGPA) formerly known as Churg-Strauss syndrome (CSS) is a vasculitic syndrome characterized by sys- temic necrotizing vasculitis of small vessels with ...
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Gingival hyperplasia as first sign of recurrence of granulomatosis with polyangiitis (Wegener’s granulomatosis): case report and review of the literature
... with polyangiitis, Wegener’s granulomatosis, gingivitis, recur- rent, recurrence” indicated only one report describing the recurrence of GPA without any oral symptoms in the initial presentation of the ...
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Granulomatosis with polyangiitis (Wegener’s) as a necrotizing gingivitis mimic: a case report
... Case presentation: An otherwise healthy 32-year-old, Caucasian woman presented to various physicians with progressive, painful oral ulcers. Following consultations with multiple primary care physicians and ...
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