Peroxisome biogenesis
The role of Pex11-beta in peroxisome biogenesis, intracellular relationship to reactive oxygen species levels and redox-sensitive cell signaling
... increase peroxisome number when overexpressed and significantly reduce peroxisome number when interrupted (Karnati and Baumgart-Vogt ...affecting peroxisome divisions indirectly (van Roermund, Tabak ...
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Arginine improves peroxisome functioning in cells from patients with a mild peroxisome biogenesis disorder
... of bile acids, the synthesis of plasmalogens and the oxi- dation of phytanic acid [1]. Peroxisome biogenesis disor- ders (PBDs) are autosomal recessive disorders characterized by an impairment in one or ...
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Identification of Six Loci in Which Mutations Partially Restore Peroxisome Biogenesis and/or Alleviate the Metabolic Defect of pex2 Mutants in Podospora
... for peroxisome biogenesis Putative X-linked adrenoleukodystrophy gene shares unexpected and has sequence similarity to the Zellweger syndrome protein homology with ABC ...
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Endoplasmic Reticulum-Associated Secretory Proteins Sec20p, Sec39p, and Dsl1p Are Involved in Peroxisome Biogenesis
... with peroxisome biogenesis and proliferation are induced during growth of yeast in oleic acid as the sole carbon source (25, 49, 50, 68, ...of peroxisome biogenesis, Pot1p showed the typical ...
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Positive Selection of Novel Peroxisome Biogenesis-Defective Mutants of the Yeast Pichia pastoris
... 247–266 bases downstream of the AOX1 stop codon, which through evolution, they have been used to identify their includes a genomic HindIII site and AOX1 terminator se- human PEX homologues in the databases, many of ...
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Heimler Syndrome is Caused by Hypomorphic Mutations in the Peroxisome Biogenesis Genes PEX1 and PEX6
... Heimler syndrome (HS) is a rare recessive disorder characterized by sensorineural hearing loss (SNHL), amelogenesis imperfecta, nail abnormalities, and occasional or late-onset retinal pigmentation. We ascertained eight ...
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Flavivirus Infection Impairs Peroxisome Biogenesis and Early Antiviral Signaling
... To further investigate the roles WNV and DENV capsid proteins play in virus-host interactions, we used affinity purification and mass spectrometry to identify capsid-binding proteins. Based on the conserved nature of ...
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Evolving models for peroxisome biogenesis.
... for peroxisome biogenesis There is overwhelming evidence in favor of a growth and division model, whereby the insertion machinery for Class1 PMPs is ...
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Peroxisome biogenesis, protein targeting mechanisms and PEX gene functions in plants
... yeasts and mammals [22]. At PEX19-1 and At PEX19-2 could also bind the Arabidopsis peroxisomal ABC transporter COMATOSE [23] which was correctly targeted to peroxisomes when expressed in S.cerevisiae [23, 24]. The human ...
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Isolation and Characterization of a New Peroxisome Deficient CHO Mutant Cell Belonging to Complementation Group 12
... for peroxisome biogenesis ...peroxisomal biogenesis disorders (PBDs) are autosomal recessive and include thirteen different known genotypes with three distinct phenotypes, Zellweger syndrome (ZS), ...
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Living-Donor Liver Transplantation From a Heterozygous Parent for Infantile Refsum Disease
... of peroxisome biogenesis characterized by generalized peroxisomal metabolic dysfunction, including accumulation of very long-chain fatty acids (VLCFAs) and phytanic acid (PA), as well as decreased ...
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Sensing and signaling for peroxisome autophagic degradation (pexophagy) in yeasts
... in peroxisome biogenesis. Thus, Pex3 is important for peroxisome biogenesis, and Pex14 – for protein import to peroxisomal ma trix (Ma and Subramani ...
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Reevaluation of the role of Pex1 and dynamin-related proteins in peroxisome membrane biogenesis
... in peroxisome biogenesis is supported by studies in many different organisms (Dimitrov et ...Upon peroxisome reintro- duction, Pex11-GFP appears in puncta with Pex13 close to the time that GFP-PTS1 ...
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Conserved and differential transcriptional responses of peroxisome associated pathways to drought, dehydration and ABA
... encoding peroxisome targeted proteins), PEX genes (involved in peroxisome biogenesis) and genes involved in plant antioxidant networks were identified in all 3 species and their expression compared ...
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The role of dynamin related proteins in vacuole biogenesis in fission yeast (Schizosaccharomyces pombe) : a thesis presented in partial fulfillment of the requirements for the degree of Master of Science in Biochemistry at Massey University, Palmerston North, New Zealand
... In the fission yeast, Schizosaccharomyces pombe, the dynamin-related proteins DRPs Vps1 and Dnm1 act redundantly in peroxisome biogenesis Jourdain et al., 2008 but nothing is known about[r] ...
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Plant peroxisomes: biogenesis and function
... modulate peroxisome morphology (Nito et ...of peroxisome biogenesis, including acting as a receptor for other PMPs and orchestrating their subsequent sorting into the pER (Karnik and Trelease, 2005; ...
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Noncanonical MicroRNA (miRNA) Biogenesis Gives Rise to Retroviral Mimics of Lymphoproliferative and Immunosuppressive Host miRNAs
... Noncanonical biogenesis of SFV miRNAs. We tested our original prediction of RNAP III-dependent transcription of the primary miRNA transcripts (pri-miRNA). The banding patterns detected via Northern blot analysis ...
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Rengstl, Birgit (2012): Biochemical characterization of an intermediate membrane subfraction in cyanobacteria involved in an assembly network for photosystem II. Dissertation, LMU München: Fakultät für Biologie
... represent biogenesis centers formed by ...the biogenesis centers in more detail and ...the biogenesis regions seem to consist of membranes surrounding the pyrenoid structure of the ...TM ...
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Peroxisome Proliferator-Activated Receptors (PPARS): A Target with a Broad Therapeutic Potential for Human Diseases: An Overview
... [69]. Peroxisome proliferator-activated receptor agonist mediated preservation of insulin/IGF responsive neurons was associated with increased expression of ChAT, which has an important role in cognition, as ...
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Peroxisome Proliferators Activated Receptor (PPAR) agonists activate hepatitis B virus replication in vivo
... Peroxisome Proliferators Activated Receptor (PPAR) agonists activate hepatitis B virus replication in vivo RESEARCH Open Access Peroxisome Proliferators Activated Receptor (PPAR) agonists activate hep[.] ...
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