polycystic kidney
Case Report: Cystinuria and Polycystic Kidney Disease
... Patient A is now a 16-year-old male from Honduras with a 6-year history of nephrolithiasis who originally presented to our institution acutely in September 2012 with a symptomatic 2-mm left ureterovesical junction ...
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Interrupted Aortic Arch in an Adult with Polycystic Kidney Disease
... dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease and is responsible for 8–10% of patients with end-stage renal ...that polycystic kidney disease ...
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Hyperuricemia and deterioration of renal function in autosomal dominant polycystic kidney disease
... dominant polycystic kidney disease; CKD: Chronic kidney disease; CKD-EPI: Chronic kidney disease epidemiology collaboration; CT: Computed tomography; ESRD: End-stage renal disease; GFR: ...
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A comparison between two semantic deep learning frameworks for the autosomal dominant polycystic kidney disease segmentation based on magnetic resonance images
... 25. Bevilacqua V, Brunetti A, Cascarano GD, Palmieri F, Guerriero A, Moschetta M. A deep learning approach for the automatic detection and segmentation in autosomal dominant polycystic kidney disease based ...
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<p>Management of Autosomal Dominant Polycystic Kidney Disease (ADPKD) During Pregnancy: Risks and Challenges</p>
... Abstract: Autosomal dominant polycystic kidney disease (ADPKD) affects up to 1 in 1000 people. The disease is characterized by the progressive development of cysts throughout the renal parenchyma due to ...
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Polycystic kidney disease
... with polycystic kidney diseases (PKDs), the kidneys contain multiple fluid-filled cysts, although other organs may also be affected ...in polycystic kidney and hepatic disease 1 (PKHD1), which ...
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A model to predict disease progression in patients with autosomal dominant polycystic kidney disease (ADPKD): the ADPKD Outcomes Model
... dominant polycystic kidney disease (ADPKD) is the most common monogenic kidney disease, and the leading inheritable cause of end-stage renal disease (ESRD) among adults [1, ...formation, ...
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Polycystic kidney disease: inheritance, pathophysiology, prognosis, and treatment
... Abstract: Both autosomal dominant and recessive polycystic kidney disease are conditions with severe associated morbidity and mortality. Recent advances in the understanding of the genetic and molecular ...
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Autosomal Recessive Polycystic Kidney Disease: A Hepatorenal Fibrocystic Disorder With Pleiotropic Effects
... Autosomal recessive polycystic kidney disease (ARPKD) is an important cause of chronic kidney disease in children. The care of ARPKD patients has traditionally been the realm of pediatric ...
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Autosomal dominant polycystic kidney disease with ectopic unilateral multicystic dysplastic kidney
... contralateral kidney, which are generally sporadic disease ...for polycystic kidney disease 1 mutation, but negative for hepatocyte nuclear factor 1 beta ...their kidney function seemed to be ...
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Standardised Outcomes in Nephrology—Polycystic Kidney Disease (SONG PKD): study protocol for establishing a core outcome set in polycystic kidney disease
... [38–40], kidney transplant- ation (SONG-Tx) [41], peritoneal dialysis (SONG-PD), and paediatric CKD (SONG-Kids) ...SONG- Polycystic Kidney Disease (SONG-PKD) project aims to establish a core outcome ...
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Modelling the long-term benefits of tolvaptan therapy on renal function decline in autosomal dominant polycystic kidney disease: an exploratory analysis using the ADPKD outcomes model
... Methods: The effect of tolvaptan on ADPKD progression was modelled by applying a constant treatment effect to the rate of renal function decline, consistent with that observed in the Tolvaptan Efficacy and Safety in ...
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Gas chromatography-mass spectrometry-based untargeted metabolomic analysis of organ tissue, plasma and urine samples from a Rat Model of polycystic kidney disease
... the kidney and liver, leading to end-stage kidney ...other polycystic kidney diseases (PKDs) is not sensitive or ...in kidney and liver tissue of the LPK rat and to investigate ...
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Polycystic Kidney Disease:The Cyst-ematic Destruction of Renal Function
... Polycystic kidney disease is the most common genetic, life-threatening disease, affecting more than ...of polycystic kidney ...of polycystic kidney disease, ARPKD, is triggered ...
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Magnetic resonance imaging is effective for evaluating the therapeutic effect of tolvaptan on total kidney volume in patients with autosomal dominant polycystic kidney disease
... dominant polycystic kidney disease (ADPKD) is a hereditary disease characterized by the progressive growth of multiple cysts in both ...both kidney enlargement and the promotion of kidney ...
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Total kidney and liver volume is a major risk factor for malnutrition in ambulatory patients with autosomal dominant polycystic kidney disease
... dominant polycystic kidney disease (ADPKD) is the most common hereditary kidney disease, and can progress to end-stage renal disease (ESRD) as kidney cysts ...
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<p>Regression of Peritubular Capillaries Coincides with Angiogenesis and Renal Cyst Growth in Experimental Polycystic Kidney Disease</p>
... Polycystic kidney disease (PKD) is the most common monogenic cause of kidney failure, and is characterised by the development of hundreds of fl uid- fi lled cysts in the kidney, which contain ...
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Urinary exosomal expression of activator of G protein signaling 3 in polycystic kidney disease
... Polycystic kidney disease (PCK) rats were obtained from a breeding colony maintained at the Medical College of Wisconsin. The PCK rat was originally identified with a spontaneous 2 base pair deletion in the ...
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Risk of intracranial hemorrhage associated with autosomal dominant polycystic kidney disease in patients with end stage renal disease
... We conducted a retrospective cohort study using the USRDS database. Because the identity of individual sub- jects is not disclosed and not obtainable from the USRDS datasets, and due to the substanial number of cases ...
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Recommendations for the use of tolvaptan in autosomal dominant polycystic kidney disease: a position statement on behalf of the ERA-EDTA Working Groups on Inherited Kidney Disorders and European Renal Best Practice
... comparable to class 1C patients in the Mayo classi fi cation of ADPKD [30]. (f ) In young ADPKD patients with CKD stage 1, the observation of ‘ no change in eGFR ’ in general is not considered a sensitive marker of slow ...
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