Primitive neuroectodermal tumors
Original Article CT and MRI manifestations of peripheral primitive neuroectodermal tumors
... Peripheral primitive neuroectodermal tumors (pPNETs) are malignant tumors with cytologi- cal and cellular genetic features that are pres- ent in the extracranial skeletal system or soft ...of ...
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MRI Features of Histologically Diagnosed Supratentorial Primitive Neuroectodermal Tumors and Pineoblastomas in Correlation with Molecular Diagnoses and Outcomes: A Report from the Children's Oncology Group ACNS0332 Trial
... 28 tumors were in pineal and 28 in nonpineal ...embryonal tumors (n ¼ 7), atypical teratoid/rhabdoid tumors (n ¼ 3), and ependymomas (n ¼ ...diagnosed primitive neuroectodermal ...
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EWS erg and EWS Fli1 fusion transcripts in Ewing's sarcoma and primitive neuroectodermal tumors with variant translocations
... We have determined the frequency of EWS fusion transcripts in a series of primary Ewing's sarcomas and peripheral primitive neuroectodermal tumors and cells lines. Type 1 and 2 EWS-Fli1 fusions were ...
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Original Article Clinical features of 12 cases with peripheral primitive neuroectodermal tumors of soft tissue
... peripheral primitive neuroectodermal tumors (pPNETs) in ...The tumors were all pPNETs of soft ...the tumors were isointense or hypo-intense on T1-weighed image (T1WI), and isointense or ...
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Benefit of Sunitinib in the treatment of pulmonary primitive neuroectodermal tumors: a case report and literature review Chunhui Zhang 1, Jingchun Zhang1 , Guangyu Wang 1, Jiajia Xu2 , Yanlin Li 2, Qing Guo 2, Tongsen Zheng1 and Yanqiao Zhang 1
... Primitive neuroectodermal tumor (PNET) is a highly aggressive small round cell tumor but is extremely rare in the ...other tumors and has been associated with response to ...
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Dynamic Susceptibility Contrast Enhanced Perfusion and Conventional MR Imaging Findings for Adult Patients with Cerebral Primitive Neuroectodermal Tumors
... DSC MR imaging provides information regarding tumor vascularity, and elevated rCBV values have been shown to correspond to areas of microvascular density and vascular endothelial hyperplasia (40). In addition, rCBV ...
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Primitive Neuroectodermal Tumors of the Brainstem: Investigation of Seven Cases
... All 7 patients died at 3 to 17 months after diagno- sis, with local recurrence in 7 and diffuse leptomen- ingeal dissemination in 6 patients. In case 1 although a reduction in tumor size was documented at the site of the ...
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Comparison of clinical features and outcomes in patients with extraskeletal vs skeletal Ewing sarcoma: an SEER database analysis of 3,178 cases
... peripheral primitive neuroectodermal tumors or Askin tumor patients who were registered in the Surveillance, Epidemiology, and End Results database from 1973 to ...
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A peripheral primitive neuroectodermal tumor originating from the pancreas: a case report and review of the literature
... Peripheral primitive neuroectodermal tumors (pPNETs) are primary malignant neoplasms, usually occurring in children or young ...cell tumors arising from primitive neuroepithelial stem ...
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Case Report Nasopharyngeal primitive neuroectodermal tumor after concurrent chemoradiotherapy for nasopharyngeal carcinoma: a case report
... Primitive neuroectodermal tumors (PNETs) belong to the class of malignant small round cell tumors, presumably of neural crest ...These tumors are highly aggressive with high mortality ...
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Low grade astrocytoma transformating primitive neuroectodermal tumour in an adult? A case report and review of literature
... Background: Supratentorial primitive neuroectodermal tumors (sPNET) are rarely occurred in adults. Only 39 cases have been reported in the past decade. The transformation from low grade to aggressive ...
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From Ataxia to Diagnosis of Askin Tumor – a Case Report
... peripheral primitive neuroectodermal tumors reveals neurosecretory granules with microtubules and ...al primitive neuroectodermal tumors are distinguished from other small, round ...
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Peripheral Primitive Neuroectodermal Tumor of Small Bowel Mesentry Presenting as Intestinal Obstruction: A Case Report.
... Peripheral primitive neuroectodermal tumors are soft tissue neoplasm’s seen in children and young ...peripheral primitive neuroectodermal tumor of ileal mesentry presenting with ...
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MicroRNAs in pediatric central nervous system embryonal neoplasms: the known unknown
... aggressive tumors with craniospinal dissemination and fatal outcome in 6 months to 1 ...are primitive neuroectodermal tumors with increased cellularity and characteristic ependymoblastic ...
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Primary primitive neuroectodermal tumor of the cervix
... Abstract: Primary primitive neuroectodermal tumors (PNETs) are rare and high-grade malignant tumors that mostly occur in children and young adults. The most common sites are the trunk, limbs, ...
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Primitive neuroectodermal tumor (PNET) of the lung in an adult woman
... Primitive neuroectodermal tumors (PNETs) are small- blue-round-cell malignancies, predominantly arising in the soft tissues or bones in children and young adults ...of tumors, based on shared ...
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First Description of a Primitive Neuroectodermal Tumor Arising in the Nose
... Primitive neuroectodermal tumors (PNETs) are a large family of tumors of neuroectodermal origin that belong to Ewing’s sarcoma family of tumors ...these tumors are rare ...
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Small Cell Ovarian Cancer in Adolescents: Report of Two Cases and Review of the Literature
... the tumors, is a component of large cells that usually represents a minor to moderate component of the tumor, but rarely can be the predominant or even exclusive component, leading to use of the descriptor “large ...
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Ewings Sarcoma Primitive Neuroectodermal Tumour Rare Extraosseous Presentation
... Ewings sarcoma family of tumours are tumours of small round cells that are morphologically similar [1] [2]. Ewings sarcoma (ES) includes Ewings of the bone [3]-[6], extraosseous Askins tumour and the primitive ...
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Medulloepithelioma, An Embryonal Tumor of the Central Nervous System, the Eye and the Optic Nerve: Review of the Clinical Behavior, Cytogenetic and Molecular Characteristics
... categorizes tumors by characteristic genetic alterations rather than histologic ...amplified tumors were also found to be characterized by high-level of expression of the microRNAs cluster contained in the ...
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