Scleroderma/Systemic Sclerosis
Smoking in Systemic Sclerosis: A Longitudinal European Scleroderma Trials and Research Group Study
... © 2018, American College of Rheumatology. This is the peer reviewed version of the following article: Jaeger, VK, Valentini, G, Hachulla, E et al. (22 more authors) (2018) Smoking in Systemic Sclerosis: A ...
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The HLA DR and DQ genes control the autoimmune response to DNA topoisomerase I in systemic sclerosis (scleroderma)
... HLA class II alleles were determined using the PCR-RFLP method in Japanese systemic sclerosis (scleroderma) patients with (n = 28) or without (n = 34) anti-topoisomerase I antibodies (anti-topo I). ...
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Cutaneous antigen stimulating lymphokine production by lymphocytes of patients with progressive systemic sclerosis (scleroderma)
... systemic sclerosis. The latter included 18 individuals with diffuse scleroderma and 12 with the CREST syndrome, a variant form of systemic sclerosis in which there is more limited ...
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Systemic Sclerosis Sine Scleroderma With Pulmonary Arterial Hypertension in a 3-Year-Old Girl
... Systemic sclerosis sine scleroderma (ssSSc) is a rare variant of systemic sclerosis, with only one pediatric case reported in the medical literature to ...
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Pressure and pain In Systemic sclerosis/Scleroderma an evaluation of a simple intervention (PISCES): randomised controlled trial protocol
... with Systemic Sclerosis (SSc)/Scleroderma have been reported to be both common and ...with Systemic Sclerosis can be improved through the provision of a simple pressure-relieving ...
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Pressure and pain In Systemic sclerosis/Scleroderma - an evaluation of a simple intervention (PISCES): randomised controlled trial protocol
... with Systemic Sclerosis (SSc)/Scleroderma have been reported to be both common and ...with Systemic Sclerosis can be improved through the provision of a simple pressure-relieving ...
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Primary myocardial disease in scleroderma – a comprehensive review of the literature to inform the UK Systemic Sclerosis Study Group cardiac working group
... This is a repository copy of Primary myocardial disease in scleroderma – a comprehensive review of the literature to inform the UK Systemic Sclerosis Study Group cardiac working group.. [r] ...
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Systemic sclerosis sine scleroderma
... Systemic sclerosis is a rare generalized disease with scleroderma, ...as systemic sclerosis sine scleroderma (ssSSc) is a very rare subset characterized by the total or partial ...
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Analysis of complement biomarkers in systemic sclerosis indicates a distinct pattern in scleroderma renal crisis
... Renal crisis is reported typically in 5–10% patents with SSc [24, 25]. Historically, this group of patients had a high risk of death (up to 85% mortality after 1 year [26]), and even after introducing treatment with ...
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Erectile dysfunction is frequent in systemic sclerosis and associated with severe disease: a study of the EULAR Scleroderma Trial and Research group
... SA, Scleroderma Center - Thomas Jefferson University, Philadelphia, PA, USA; Zenone T, Unit of Internal Medicine, Valence, France; Pileckyte M, Hospital of Lithuanian University of Health Sciences Kauno Klinikos, ...
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Von Willebrand factor propeptide as a marker of disease activity in systemic sclerosis (scleroderma)
... Systemic sclerosis (SSc) is characterized by autoimmu- nity, microangiopathy, and fibrosis in skin and internal organs. Endothelial activation is reflected by increased amounts of circulating endothelial ...
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Atypical clinical presentation of a subset of patients with anti RNA polymerase III non scleroderma cases associated with dominant RNA polymerase I reactivity and nucleolar staining
... in systemic rheumatic diseases are useful biomarkers associated with certain diagnoses and/or clinical manifestations ...with scleroderma (systemic sclerosis, SSc); some are considered highly ...
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Systemic sclerosis medications and risk of scleroderma renal crisis
... Scleroderma Renal Crisis (SRC) develops abruptly in sys- temic sclerosis (SSc) and is associated with significant morbidity and mortality [1 – 4]. Proteinuria, anemia, thrombocytopenia, elevated erythrocyte ...
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Primary myocardial disease in scleroderma – a comprehensive review of the literature to inform the UK Systemic Sclerosis Study Group cardiac working group
... Cardiac involvement is reported in both disease subtypes although more frequently in dcSSc (see Table 3) [60-64]. In the study by Ferri et al, 23% of lcSSc and 32% of dcSSc (p=0.05) had cardiac involvement at diagnosis ...
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Vascular involvement in systemic sclerosis (scleroderma)
... vasculopathy, systemic autoimmunity (autoantibodies and T cell autoantigen reactivity) and ...and scleroderma renal crisis are more commonly associated with ...sine scleroderma” is also recognized, ...
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Treatment outcome in early diffuse cutaneous systemic sclerosis: the European Scleroderma Observational Study (ESOS).
... Contributors ALH, ML, RH, LM, AS, EB, LC, JHWD, OD, KF, WJG, RO, MV and CPD were members of the Steering Committee and designed the study. ALH, RH, LM, LC, JHWD, OD, MV, CA, VHO, DF, MH, MM-C, AB-G,OM, ACJ, PJ, WS, PM, ...
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Treatment outcome in early diffuse cutaneous systemic sclerosis: the European Scleroderma Observational Study (ESOS)
... Contributors ALH, ML, RH, LM, AS, EB, LC, JHWD, OD, KF, WJG, RO, MV and CPD were members of the Steering Committee and designed the study. ALH, RH, LM, LC, JHWD, OD, MV, CA, VHO, DF, MH, MM-C, AB-G,OM, ACJ, PJ, WS, PM, ...
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Clinical significance of antibodies to Ro52/TRIM21 in systemic sclerosis
... SLE: systemic lupus erythematosus; Sm: Smith autoantigen; SPAP: systolic pulmonary artery pressure; SS-A: Sjögren syndrome antigen A or Ro; SS-B: Sjögren syndrome antigen B or La; SSc: systemic ...
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Endothelial cell apoptosis is a primary pathogenetic event underlying skin lesions in avian and human scleroderma
... with systemic sclerosis (SSc), localized scleroderma, or ke- loids, and at the initial disease stage in the University of California at Davis (UCD) lines 200/206 chickens, which develop a hereditary ...
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A Study of Cardio Pulmonary Manifestations in Systemic Sclerosis
... to scleroderma may be found in the writings of Hippocrates as far back as 460–370 ...a scleroderma-like disease was published by Carlo Curzio in Naples in ...term scleroderma, as the skin was the ...
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