motor neuron
IPLEX Administration Improves Motor Neuron Survival and Ameliorates Motor Functions in a Severe Mouse Model of Spinal Muscular Atrophy
... enhance motor neuron sur- vival in SOD1/G93 mouse model of amyotrophic lateral sclerosis (ALS), de- laying the progression of the disease ...spinal motor neuron survival and axon outgrowth ...
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Cholestenoic acids regulate motor neuron survival via liver X receptors
... of motor neurons in vivo has been ...regulate motor neuron function, we delved deeper into the human CSF sterolome and examined plasma of patients with 2 different human diseases associated with ...
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Evaluation of function, disability and participation of patients with motor neuron disease
... Table 1 documents all discovered assessments to estimate general health and specific disturbances in polio patients [1, 3–30]. Specific health assessments as well as general health assessments are included. It can be ...
8
Dominantly Inherited Amyotrophic Lateral Sclerosis (Motor Neuron Disease)
... The term amyotrophic lateral sclerosis (ALS) was first introduced by Charcot to describe cases with mixed upper and lower motor neuron signs without.. This is paper #46 f[r] ...
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Vitamin E deficiency and risk of equine motor neuron disease
... in motor neuron death but not necessarily the sole etiologic agent/ ...the motor neuron disease and may be able to provide new therapeutic avenues either by amelioration of the etiologic ...
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Cervicothoracic Intradural Arachnoid Cyst Misdiagnosed as Motor Neuron Disease
... Another essential precondition for a diagnosis of ALS is the “progressive spread of symptoms or signs within a region or to other regions, as determined by history or examination” [2]. This criterion is pivotal since ...
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Motor neuron M3 controls pharyngeal muscle relaxation timing in Caenorhabditis elegans
... GREEN motor neuron kill, since neither MC nor M4 has been observed to have any effect on the slippery phenotype in any combination (Avery and Horvitz, ...as motor neurons those neurons that had ...
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Marchiafava-Bignami disease mimics motor neuron disease: case report
... lower motor neuron signs, the initial diagnosis was motor neuron ...primary motor cortices ...mimic motor neuron disease ...
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Neurophysiological evaluation of bladder dysfunction in lower motor neuron lesions
... terminal motor latency, sacral reflexes, and pudendal nerve somatosensory-evoked potentials in bladder ...Lower motor neuron lesions selected from Tanta and Alexandria University ...terminal ...
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MYOMIRNAS ROLE IN ALS SUGGEST A CROSSTALK BETWEEN MUSCLE AND MOTOR NEURON
... lower motor neurons in the spinal cord or brainstem and upper motor neurons in the motor ...of motor neurons leads to muscle atrophy and weakness, fasciculations, and spasticity ...of ...
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Decreased function of survival motor neuron protein impairs endocytic pathways.
... DA motor neurons of smn-1(ok355) animals only: SYD-2 (α-liprin), NLP-21 (GGARAF neuropeptide family) and APT-4 (AP2 ...no motor neuron death ...
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Neurobiology of axonal transport defects in motor neuron diseases: Opportunities for translational research?
... dominant motor function defects and motor neuron degeneration in the Legs at odd angles (Loa) and Cramping 1 (Cra1) mouse strains (Hafezparast et ...cord motor neurons by E18. Cultured ...
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Oligodendrocytes contribute to motor neuron death in ALS via SOD1 dependent mechanism
... before cell death was detectable. Electrophysiological recordings were performed at day 7 post MN seeding. This time point was chosen to allow MN maturation and at the same time to determine if MN distress could be ...
25
Tardbpl splicing rescues motor neuron and axonal development in a mutant tardbp zebrafish
... in motor neuronal de- velopment, therefore establishing a vital role for Tardbp in motor neuron and axon ...of motor neuron disease and in sod1 mouse models of ALS ...than motor ...
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Study on treatment method of motor neuron disease based on Jiweiling injection
... the motor neuron disease, the medicine mentioned above can prolong the disease course of this disease, the symptoms of patients has no significant improvement, and generally the adverse reactions can ...
5
Post polio Syndrome: More Than Just a Lower Motor Neuron Disease
... Quantitative motor test; rCT, randomized controlled trial; RDBPC, Randomized double-blind placebo controlled; REE, resting energy expenditure; RLS, Restless leg syndrome; RNA, Ribonucleic acid; RQ, respiratory ...
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Process evaluation and exploration of telehealth in motor neuron disease in a UK specialist centre
... This is a repository copy of Process evaluation and exploration of telehealth in motor neuron disease in a UK specialist centre White Rose Research Online URL for this paper http //eprints whiterose a[.] ...
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The Effects of Two Different Stretching Programs on Balance Control and Motor Neuron Excitability
... Flexibility and balance are considered to be important for health and physical fitness. Flexibility affects muscular performance (e.g. Ferreira, Teixeira-Salmela, & Guimarães, 2007). It was shown that subjects with ...
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Identification and outcomes of clinical phenotypes in amyotrophic lateral sclerosis/motor neuron disease: Australian National Motor Neuron Disease observational cohort
... lower motor neuron signs. Patients with combined upper and lower motor neuron signs in one segment with at least one other segment involved with either upper motor neuron (UMN) ...
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Turkish families with juvenile motor neuron disease broaden the phenotypic spectrum of SPG11
... Conclusions: Four patients with juvenile-onset motor neuron disease with consanguineous parents were found to carry homozygous mutations in the SPG11 gene. Our findings confirm the overlapping phenotypes of ...
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