Sickle cell
Sickle Cell Beta Thalassemia: A Rare Entity
... On extra oral examination, pallor and yellowish discoloration of the skin over the face and yellowish tint of both the sclera were noted. Other findings included bimaxillary protrusion, lip incompetence and features of ...
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Cutaneous Manifestations of Sickle Cell Disease
... Lower extremity ulcers in sickle cell patients are difficult to treat and often recur with discontinuation of therapy. Healing of these ulcers occurs 20 times more slowly than healing of similar types of ...
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A pilot test of the Adult Sickle Cell Quality of Life Measurement Information System (ASCQ-Me) and the Jenerette Self-Care Assessment (J-SAT) Tools in adults with sickle cell disease
... Our sample ( n = 20) had a similar race, sex, age, and SCD genotype (> 50% = HbSS) breakdown to the refer- ent population. While our sample was recruited from a SCD clinic and conference, respondents in the referent ...
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Sickle cell disease and pregnancy outcomes: a study of the community-based hospital in a tribal block of Gujarat, India
... maintained since 2003. The data pertain to four and half years from March 2011 to September 2015; SCD information was not widely collected before March 2011. The data entry operators enter the hospital register ...
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Concurrent sickle cell anemia and alpha thalassemia Effect on pathological properties of sickle erythrocytes
... of sickle cell disease. The irreversibly sickled cell number, proportion of very dense sickle RBC, and diminished deformability of sickle RBC each varied directly with alpha-globin gene ...
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Oxidative Modification of Lipids and Lipoproteins in Steady State Sickle Cell Anemic Patients from South-Eastern Nigeria
... in sickle cell disease where these conditions are equally obtainable when the patients are in crisis, it is expected that oxidative degradation of lipoproteins is a possibility or even a ...the ...
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Significant Reduction of Vitamin B12 Levels in Sudanese Sickle Cell Disease Patients
... in sickle cell patients; however others factor also might be has a role in cobalamin defi- ciency such as decreased cobalamin production by stomach or decreased absorption from the ileum due to the crisis ...
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Health-related quality of life of adolescents with sickle cell disease in sub-Saharan Africa: a cross-sectional study
... A number of disease-related factors have been found to affect quality of life (QoL) in children with SCD such as vulnerable socioeconomic status, age of the patient by physical manifestations of SCD notably in the form ...
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OXYGEN DISSOCIATION CURVES IN SICKLE CELL ANEMIA AND IN SUBJECTS WITH THE SICKLE CELL TRAIT
... Table I indicates that despite efforts to keep the pCO2 constant in all studies, the mean pCO2 for the experimental points calculated in the cases of sickle cell anemia was higher than t[r] ...
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Study of clinical profile of painful crisis in hospitalized children of sickle cell anemia
... 21. Jones S, Duncan ER, Thomas N, Walters J, Dick MC, Height SE, et al. Windy weather and low humidity are associated with an increased number of hospital admissions for acute pain and sickle cell disease ...
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Amelioration of Sickle Cell Pain after Parathyroidectomy in Two Patients with Concurrent Hyperparathyroidism: An Interesting Finding
... 2.1. Case Report 1. Our first case is a 59-year-old female patient who moved to USA from Haiti two years ago with a diagnosis of sickle cell-beta + thalassemia. She reported having generalized pain almost ...
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Critical realism, agency and sickle cell : case studies of young people with sickle cell disorder at school
... 2010 Sickle Cell Disease Association of America Annual Conference, the audience consensus was that the negative experiences of young people with SCD at school in England (Dyson et al, 2010) were also ...
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Growth and metabolism in homozygous sickle cell disease
... All cohort children were initially seen at the sickle cell clinic at three monthly intervals coinciding with their birthdays. (The schedule was changed to 6 monthly visits in AA subjects at age 5 years to ...
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The Effect of Hydroxyurea Treatment on Fetal Haemoglobin Level and Clinical Status of Sudanese Sickle Cell Anaemia Patients
... Sudanese sickle cell anaemia, this can be attributed to many factors reported to influence the response to hydroxurea treatment such as the baseline level of Hb-F as the higher response of Hb-F level has ...
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Influence of glucose-6 phosphate dehydrogenase (G6-PD) deficiency upon clinico-haematological and biochemical expression of patients with sickle cell disease
... and sickle cell genes on one hand and environment on the other, one may therefore expect changes in their frequencies over a period of time in the ...of sickle cell ...
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Sickle Cell Disease: A Question of Equity and Quality
... specialized sickle cell disease-related care, which does not, unfortunately, apply to every child with sickle cell disease in the United ...
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“HÉMODYA”: A PHYTOMEDECINE FOR SICKLE CELL DISEASE MANAGEMENT IN CAMEROON
... The present study, evaluates the role of “hémodya” as a phytomedicine in the management of sickle cell disease. The phenolic content, free radical, and reactive oxygen scavenging ability of “hémodya” were ...
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Effectiveness of Hydroxyurea Therapy in Sickle Cell Disease and Sickle Cell Trait
... of sickle cell disease (SS) and trait (AS), fulfilling all eligibility criteria, attending general medicine, sickle cell OPD and medicine wards were included after obtaining written informed ...
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Parental Influence on Sickle Cell Crisis among Patients Attending Secondary Facilities in Abeokuta South Local Government Area, Ogun State
... of sickle cell disease as most still belief it’s a form of bone disease that affect the child especially during the cold ...preventing sickle cell ...of sickle cell crisis is ...
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Combination of Haemoglobinopathy and Haemopathy —(Adult T Cell Lymphoma/Leukemia and Sickle Cell Disease: A Rare Case of Disease Observed in the Adult Referral Center of Sickle Cell Disease (CRD A) in Martinique
... Authors report a case of beta thalassemia combined with hematological ma- lignant (ATLL) in a 40-year-old female, cashier screened HTLV-1 positive; followed since her 10 years old for the account of ...
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